True about 'Tetralogy of Fallot' (TOF) are all of the following EXCEPT?
TETRALOGY OF FALLOT: --> MC congenital cyanotic hea disease in children --> Contain 4 COMPONENTS: 1. Large, unrestricted VSD 2. Pulmonary infundibular stenosis 3. Overriding aoa 4. Right ventricular hyperophy --> CLINICAL FEATURES: Cyanosis Clubbing Polycythemia Cyanotic spells Hea failure is not seen in TOF, unless it is complicated by Anemia /Infective endocarditis /Myocarditis / Systemic hypeension Severity of cyanosis is directly propoional to the severity of pulmonary stenosis; while intensity of murmur is inversly propoional to severity of pulmonary stenosis During cyanotic spell, murmur decreases or becomes absent -Ostium primum type ASD: It is situated in the lower poion of atrial septum and overlies mitral and tricuspid valves. Left axis detion is seen in ostium primum ASD due to RV conduction defect. - Ostium secundum is most common type of ASD - SYNDROMES ASSOCIATED WITH ASD 1. Pierre Robin Sequence 2. TAR Syndrome 3. Fetal Alcohol syndrome 4. Ehler Danlos Syndrome 5. Down Syndrome 6. Holt-Oram syndrome 7. Ellis van Creveld Syndrome 8. Rubinstein Taybi syndrome