Susac syndrome is a rare, microangiopathic disorder characterised by Susac syndrome is a Description A reference to the effectiveness encephalopathy, hearing loss and retinal artery branch occlusions. Case reports rare, microangiopathic and of plasma exchange has been show benefit of IVIg or plasma exchange in combination with corticosteroids, disorder characterised Diagnostic included. generally with, or in mild cases without, other immunosuppressive agents. by encephalopathy, Criteria hearing loss and retinal artery branch occlusions. Case reports show benefit of intravenous immunoglobulin (IVIg) therapy in combination with corticosteroids, with or without other immunosuppressive agents Diagnosis is Yes By which specialty Neurologist This condition must now be required diagnosed by a specialist in Immunologist neurology, immunology, Rheumatologist rheumatology or ophthalmology as this condition is rare and Ophthalmologist usually managed by these specialists. Diagnosis No By which specialty must be verified Exclusion No change
Description and Diagnostic Criteria Susac syndrome is a rare, microangiopathic disorder characterised by encephalopathy, hearing loss and retinal artery branch occlusions. Case reports show benefit of intravenous immunoglobulin (IVIg) therapy in combination with corticosteroids, with or without other immunosuppressive agents Susac syndrome is a rare, microangiopathic disorder characterised by encephalopathy, hearing loss and retinal artery branch occlusions. Case reports show benefit of IVIg or plasma exchange in combination with corticosteroids, generally with, or in mild cases without, other immunosuppressive agents. A reference to the effectiveness of plasma exchange has been included. Diagnosis is required Yes By which specialty Neurologist Immunologist Rheumatologist Ophthalmologist This condition must now be diagnosed by a specialist in neurology, immunology, rheumatology or ophthalmology as this condition is rare and usually managed by these specialists. Diagnosis must be verified No By which specialty Exclusion No change
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