AORTIC CONGENITAL HEART DISEASE 2002 Cardiovascular Conference Report Recommendation Tables, Page 122 PHYSIOLOGY/ DIAGNOSIS CERTIFICATION RE-CERTIFICATION FUNCTIONAL Bicuspid Aortic Valve May result in aortic See section on Valvular See section on Valvular stenosis or regurgitation Diseases. Diseases. (see section on Valvular Diseases), aortic root No if: enlargement, aortic Aortic transverse aneurysm formation and diameter > 5.5 cm. aortic rupture. Yes if: Annual Surgical intervention successfully performed. Subvalvular Aortic Mild = favorable Yes if: Annual Stenosis Has potential for No valvular abnormality Evaluation by cardiologist progression. or hypertrophic knowledgeable in adult cardiomyopathy. congenital heart disease is require. Moderate or severe = No if: unfavorable. Symptomatic and mean pressure gradient >30 mm Hg. Yes if: Annual At least 3 months after Evaluation by cardiologist successful surgical knowledgeable in adult resection when cleared by congenital heart disease cardiologist required, including knowledgeable in echocardiogram. congenital heart disease. Discrete Supravalvular Unfavorable prognosis No, unless surgery. Aortic Stenosis due to associated coronary and aortic Yes if: Annual disorder. At least 3 months post Evaluation by cardiologist surgical intervention; knowledgeable in adult Cleared by cardiologist congenital heart disease is knowledgeable in adult recommended. congenital heart disease.
AORTIC CONGENITAL HEART DISEASE 2002 Cardiovascular Conference Report Recommendation Tables, Page 122 DIAGNOSIS PHYSIOLOGY/ FUNCTIONAL CERTIFICATION RE-CERTIFICATION Bicuspid Aortic Valve May result in aortic stenosis or regurgitation (see section on Valvular Diseases), aortic root enlargement, aortic aneurysm formation and aortic rupture. See section on Valvular Diseases. No if: Aortic transverse diameter > 5.5 cm. Yes if: Surgical intervention successfully performed. See section on Valvular Diseases. Annual Subvalvular Aortic Stenosis Mild = favorable Has potential for progression. Moderate or severe = unfavorable. Yes if: No valvular abnormality or hypertrophic cardiomyopathy. No if: Symptomatic and mean pressure gradient >30 mm Hg. Yes if: At least 3 months after successful surgical resection when cleared by cardiologist knowledgeable in congenital heart disease. Annual Evaluation by cardiologist knowledgeable in adult congenital heart disease is require. Annual Evaluation by cardiologist knowledgeable in adult congenital heart disease required, including echocardiogram. Discrete Supravalvular Aortic Stenosis Unfavorable prognosis due to associated coronary and aortic disorder. No, unless surgery. Yes if: At least 3 months post surgical intervention; Cleared by cardiologist knowledgeable in adult congenital heart disease. Annual Evaluation by cardiologist knowledgeable in adult congenital heart disease is recommended.