Completion Date: 2014. The spire of One WTC attains a height of exactly 1,776 feetâa shout-out to the birth year of the United States. The building proper is only around 1,300 feet tall, but the CTBUH chose to count spire toward the building's official height.
Although Batten disease is the juvenile form of NCL, most doctors use the same term to describe all forms of NCL. Early symptoms of Batten disease (or NCL) usually appear in childhood when parents or doctors may notice a child begin to develop vision problems or seizures. In some cases the early signs are subtle, taking the form of personality and behaviour changes, delayed speech, slow learning, clumsiness or stumbling.
The International Batten Disease Consortium (1995) reported a Finnish patient with Batten disease confirmed by identification of compound heterozygosity for 2 deletions in the CLN3 gene (607042.0001; 607042.0002). After a normal birth and early childhood, he developed failing vision at age 6.5 years.