There are countless reports of vascular complications resulting from vascular fragility in patients with Ehlers-Danlos syndrome. Table 2 lists the arterial complications described in studies of a total of 231 patients that were identified in a literature review. More than half of these patients had aneurysms, generally multiple and frequently in visceral arteries. However, it should be noted that there is also a risk of arterial rupture in vessels that do not have aneurysms and these can be spontaneous or caused by minimal traumas.3