Anti-BP230 antibodies were found in the serum of 44 BP patients (47.3%) with a mean titer of 29.1 ± 37 U/mL (Table 3). Interestingly, 39 BP patients without mucosal involvement (52%) but only 5 among BP patients with mucosal involvement (27.8%) had a positive anti-BP230 ELISA value (P = 0.06). Such a difference tendency was also observed when analyzing the anti-BP230 mean titer (32.2 ± 37.8 and 16.2 ± 30.9 U/mL; P = 0.07, respectively) (Table 3). At baseline, anti-BP230 antibody serum concentrations were correlated with none of the BPDAI scores within these two groups (Table 4B).