But Threnody explains that her presence at the castle caused her father to dote on her and neglect his duties to the destruction of the kingdom; her stepmother had merely made her destructive potential literal, and forced her to confront what she was doing.The character of the evil stepmother can also be found in the genre of young adult fiction or young adult social problem novels. In Lisa Heathfields Paper Butterflies. the protagonist June suffers horrific abuse at the hands of her stepmother, a fact that she conceals from her father. Despite many examples of evil or cruel stepmothers, loving stepmothers also exist in fiction. In Kevin and Kell, Kell is portrayed as loving her stepdaughter Lindesfarne, whom her husband Kevin had adopted during his previous marriage. Likewise, Lindesfarne considers Kell her mother, and has a considerably more favorable view of her than Angelique, Kevins ex-wife and her adoptive mother, due to feeling neglected by Angelique during her childhood. The Disney film Enchanted also makes references to the "evil stepmother" belief, as the villainess is a stepmother, but her wickedness comes from her selfishness and power hungriness rather than the simple fact she is a stepmother. When a little girl tells the heroine Giselle that all stepmothers are evil, Giselle reminds her that she personally knows some wonderful women who were good stepmothers, and the fact a woman is a stepmother does not suddenly change her personality.
Incomplete conversion of the sulfhydryl –SH group onto S-S disulfide bonds in the protein of the cortical fibers leads to cortical softness and subsequent invagination of the fully keratinized distal hair shaft into the softer, abnormally keratinized proximal hair shaft. Intussusception of the distal hair shaft into the proximal hair shaft results in a distinctive ball-and-socket hair shaft deformity. The affected hairs are brittle and breakage is common, resulting in short hairs.Migratory lesions of ichthyosis linearis circumflexa may be caused by a dermal influx of inflammatory cells that undergo phagocytosis and digestion by keratinocytes, resulting in disruption of keratinization.Increased transepidermal water loss resulting from the disturbance of corneocyte barrier function in erythroderma may cause profound metabolic abnormalities and hypernatremia, particularly in neonates. Epidemiology
Approximately 200 cases of trichorrhexis invaginata (bamboo hair) have been reported in the literature, but the true incidence is not known. The incidence of trichorrhexis invaginata (bamboo hair) may be as high as 1 case in 50,000 population. Girls are affected more often by trichorrhexis invaginata (bamboo hair) than boys, but is present in all races. History
In 1937, Touraine and Solente first noted the association between hair-shaft defects (bamboo node) and ichthyosiform erythroderma. Còme first coined the term ichthyosis linearis circumflexa in 1949, although Rille had previously recorded the distinctive features of ichthyosis linearis circumflexa by 1922. In 1958, Netherton described a young girl with generalized scaly dermatitis and fragile nodular hair-shaft deformities, which he termed trichorrhexis nodosa.