Informing patients and caretakers has resulted in decreased corneal scarring and need for more aggressive surgical measures such as tarsorrhaphy, conjunctival flaps, and corneal transplants. Prognosis
Average age of death is in the 3rd decade of life, however, affected persons may live into the 7th decade of life. Death occurs in 50% of the affected individuals by age 30. The outlook for patients with FD depends on the particular diagnostic category. Patients with chronic, progressive, generalized dysautonomia in the setting of central nervous system degeneration have a generally poor long-term prognosis. Death can occur from pneumonia, acute respiratory failure, or sudden cardiopulmonary arrest in such patients.The survival rate and quality of life have increased since the mid-1980s mostly due to a greater understanding of the most dangerous symptoms. At present, FD patients can be expected to function independently if treatment is begun early and if major disabilities are avoided. Epidemiology
Familial dysautonomia is seen almost exclusively in Ashkenazi Jews and is inherited in an autosomal recessive fashion. Both parents must be carriers in order for a child to be affected. The carrier frequency in Jews of Eastern and Central European (Ashkenazi) ancestry is about 1/30, while the carrier frequency in non-Jews is unknown. If both parents are carriers, there is a one in four, or 25%, chance with each pregnancy for an affected child.
Others liken the pain and sensation to a chemical burn that doesnt go away. It is a mistake to think that the reaction is like a sunburn, it is far deeper in the skin and often requires the use of ingestible steroids as well as topical steroids in order to alleviate the condition to a degree. The best protection is to be fully covered from sunlight, even when cloudy or hazy. The use of UV-rated clothing is suggested as well as a UV-rated umbrella for outdoors. See also
List of cutaneous conditions
Photosensitivity with HIV infection
Skin lesion

References


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