ulnar nerve, 2 cases) or median nerve, 1 case), hip/lower limb (i.e. sciatic nerve, 1 case), and lumbar spine/pelvis/thigh (i.e. the obturator nerve, 1 case). Individual cases of NF have been reported to occur in the lower female genital tract, bladder, prostate, tongue, and parotid gland. In some cases, NF tumors have  regressed after incisional biopsy, i.e. a biopsy that takes a small part of the diseased tissue.The cranial fasciitis variant of NF occurs in the soft and hard cranial tissues of the outer layers of the skull. Patients with this variant are more commonly males than females and almost exclusively between 3 weeks and 6 years of age. They typically present with a tumor in areas of the head that lay directly over the temporal or parietal bones. Individual cases have been reported to occur in the lower jaw, frontonasal region, anterior nasal spine (i.e. nasal process of the maxilla), and the orbit (i.e. eye socket)-maxilla area. Characteristically, the tumor is rapidly enlarging, non-painful, rarely regressing without treatment, and potentially expanding into the skulls interior.In a review of 50 cases, the intravascular fasciitis variant of NF occurred in individuals aged 6 months to 66 years (median age 27 years) with male and females being equally affected (52%:48%). Individuals with this variant commonly presented with a blood vessel-localized tumor of the head and neck area (34% of cases), lower extremity (32% of cases), upper extremity (20% of cases), or trunk (14% of cases).
spread of tumor to different parts of the body) that along with the primary tumor site were partially controlled with radiation therapy. The other case was treated by wide surgical resection of the tumor; this case did not have metastatic disease and one year after the wide resection had no recurrences. See also
Leiomyosarcoma
List of cutaneous conditions
Inflammatory myofibroblastic tumour

References


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