Phakomatosis pigmentokeratotica
Phakomatosis pigmentokeratotica is a rare neurocutanous condition  characterized by the combination of an organoid sebaceous nevus and speckled lentiginous nevus.: 634–5 : 776  It is an unusual variant of  epidermal naevus syndrome. It was first described by Happle et al. It is often associated with neurological or skeletal anomalies such as hemiatrophy, dysaesthesia and hyperhidrosis in a segmental pattern, mild mental retardation, seizures, deafness, ptosis and strabismus.

See also
Skin lesion
List of cutaneous conditions associated with increased risk of nonmelanoma skin cancer

References


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