It was first identified in March 1996 in the UK, when 10 cases of a new disease with neurological symptoms were reported and soon associated with the Bovine Spongiform Encephalopathy (BSE),  “mad cow ”-disease.

                Prvič je bila odkrita v Združenem kraljestvu marca 1996, ko so poročali o 10 primerih nove bolezni z nevrološkimi simptomi in jo povezali z bovino spongiformno encefalopatijo (BSE), boleznijo 
                „
                norih krav
                “
                .
            