A 5-year-old girl with a patch of kinky hair in the right parietal region, which had been present since the age of 4 months and different colored eyes since birth referred to our clinic []. The underlying scalp was normal. The affected hair appeared smaller in diameter and lighter than the normal hair color and no structural hair abnormalities were detected under the light microscope. She had slightly hyperpigmented linear lesions mostly marked on the anterolateral of the right arm with midline pectoral and abdominal extension []. The right eye was diffusely brown, and the left was green []. No ophthalmologic, cardiac, neurological or skeletal abnormalities were observed. Nails and teeth were normal. The patient was diagnosed with a woolly hair nevus of the right parietal scalp associated pigmented demarcation lines and heterochromia iridis.
We present a 3-year-old healthy girl, whose mother was concerned about recent hair changes. The patient had no personal or family history of cutaneous diseases. At physical exam, the girl had a phototype II skin, normal teeth and nails. The back of the scalp revealed a well-circumscribed patch of kinky, curly light blonde hair. The rest of the physical exam was normal. Dermoscopy was not performed at the time.\nWoolly hair nevus was diagnosed. The parents were counseled about the benign and chronic nature of this lesion. Ophthalmologic evaluation was recommended, but the parents of the patient refused. No further studies were performed [Figures and ].