A 33-year-old female presented 3 months postpartum with a headache of moderate severity and progressive visual loss in both eyes. On examination, the patient's Glasgow coma scale (GCS) was 15/15. Visual field examination showed left homonymous incomplete hemianopia. Her visual acuity was 20/25 in the right eye and 20/30 in the left eye. Her discs and macula were healthy bilaterally. Extraocular movements were intact and pupils were reactive. The rest of her examination was unremarkable. Complete endocrine workup was normal.\nMagnetic resonance imaging (MRI) revealed a large heterogeneous, hyperintense, hemorrhagic right suprasellar extra-axial complex cystic structure measuring 31 × 30 × 90 mm on T1-weighted images. There was mass effect on the adjacent hypothalamus and third ventricle displacing them toward the left and superiorly in addition to the optic pathway. The pituitary stalk was displaced toward the left. The lesion encased the right posterior cerebral artery and displaced the right carotid artery laterally []. Computed tomography (CT) arteriography demonstrated a completely thrombosed center. The imaging findings were compatible with suprasellar CM.\nThe patient underwent right frontal craniotomy and gross total resection of her suprasellar intrachiasmatic large infiltrative hemorrhagic CM. Organizing blood clots with reactive fibrohistiocytic and inflammatory reaction admixed with some ectatic vascular channels suggestive of a vascular malformation were noted. There were small foci admixed with granulation tissue, showing some dilated cavernous spaces that would be compatible with a vascular malformation such as cavernous angioma. On immunohistochemistry, the lesion was CD163+, CD20 rare, CD3+, CD34+, CD31+, CD38+, CTK−, EMA plasma cells, GFAP−, S100 dendritic cells, SMA vascular smooth muscle.\nThe patient had an uneventful operative course. Her visual acuity improved to 20/20 in both eyes. Extraocular muscles showed mild limitation of both eyes in an upward gaze. Otherwise, she was stable with no neurological deficits. Follow-up MRI at 12 months revealed complete removal of the suprasellar hemorrhagic CM with no evidence of a residual lesion or recurrence [].
A 16-year-old boy presented progressive visual disturbance that started 5 months prior with headache. The headache had subsided; however, the visual symptoms persisted. His visual acuity was 0.02 in his left eye and 0.3 in his right eye. The Goldmann perimetry field test revealed a large central scotoma of his left eye field and a temporal hemianopsia of his right eye field (). Brain MR imaging showed a heterogeneous hemorrhagic mass in the optic chiasm, extending posteriorly along the bilateral optic tracts with no definitive contrast enhancement (). The presumptive diagnosis was an unusual CM involving the optic pathway. Following left pterional craniotomy and sylvian dissection, the optic chiasm, which was mottled with dark dots, was visualized. A small window was made on the lateral side of the optic chiasm. Chocolate-colored tissue mixed with old blood was partially evacuated (). The pathology report confirmed the diagnosis of CM. Following surgery, the patient's visual acuity in his left eye slightly improved (0.03/0.3). The central scotoma of his left eye field had resolved; however, he subsequently acquired a nasal hemianopsia in his left eye field. At the patient's 2-year follow-up, there were no episodes of headache, visual change, or documented bleeding on serial MR imaging ().