A 5-year-old girl child presented with abnormal patch of hair since 2 years of age. Her parents noticed a single patch of curling and coiling of hair along with altered texture over the left side of scalp. Her parents felt the patch to be unruly and unsightly and hence attempted repeated tonsuring. In spite of this, the patch of hair remained the same. Birth and development history of the child was normal. Her family members did not have similar complaints. On examination, we noticed a solitary circumscribed patch of size 6×4 cm located over the left frontoparietal region of scalp. The hair over the patch had an altered texture, was lighter in color, thinner, tightly coiled, and curled giving an unkempt appearance []. The skin over the patch was apparently normal. Examination of rest of the scalp, teeth and nails were also normal. There was no evidence of palmoplantar keratoderma and evidence of any epidermal nevus elsewhere. Ophthalmic and cardiac evaluation did not reveal any abnormality. There was no evidence of precocious puberty. Based on the above findings, we arrived at a diagnosis of localized woolly hair nevus. Hair microscopic examination showed non-specific features. Scalp biopsy revealed normal hair follicles and appendages []. Routine hemogram, serum biochemistry, electrocardiogram and echocardiogram were normal.
We present a 3-year-old healthy girl, whose mother was concerned about recent hair changes. The patient had no personal or family history of cutaneous diseases. At physical exam, the girl had a phototype II skin, normal teeth and nails. The back of the scalp revealed a well-circumscribed patch of kinky, curly light blonde hair. The rest of the physical exam was normal. Dermoscopy was not performed at the time.\nWoolly hair nevus was diagnosed. The parents were counseled about the benign and chronic nature of this lesion. Ophthalmologic evaluation was recommended, but the parents of the patient refused. No further studies were performed [Figures and ].