A 5-year-old girl child presented with abnormal patch of hair since 2 years of age. Her parents noticed a single patch of curling and coiling of hair along with altered texture over the left side of scalp. Her parents felt the patch to be unruly and unsightly and hence attempted repeated tonsuring. In spite of this, the patch of hair remained the same. Birth and development history of the child was normal. Her family members did not have similar complaints. On examination, we noticed a solitary circumscribed patch of size 6×4 cm located over the left frontoparietal region of scalp. The hair over the patch had an altered texture, was lighter in color, thinner, tightly coiled, and curled giving an unkempt appearance []. The skin over the patch was apparently normal. Examination of rest of the scalp, teeth and nails were also normal. There was no evidence of palmoplantar keratoderma and evidence of any epidermal nevus elsewhere. Ophthalmic and cardiac evaluation did not reveal any abnormality. There was no evidence of precocious puberty. Based on the above findings, we arrived at a diagnosis of localized woolly hair nevus. Hair microscopic examination showed non-specific features. Scalp biopsy revealed normal hair follicles and appendages []. Routine hemogram, serum biochemistry, electrocardiogram and echocardiogram were normal.
A 5-year-old girl with a patch of kinky hair in the right parietal region, which had been present since the age of 4 months and different colored eyes since birth referred to our clinic []. The underlying scalp was normal. The affected hair appeared smaller in diameter and lighter than the normal hair color and no structural hair abnormalities were detected under the light microscope. She had slightly hyperpigmented linear lesions mostly marked on the anterolateral of the right arm with midline pectoral and abdominal extension []. The right eye was diffusely brown, and the left was green []. No ophthalmologic, cardiac, neurological or skeletal abnormalities were observed. Nails and teeth were normal. The patient was diagnosed with a woolly hair nevus of the right parietal scalp associated pigmented demarcation lines and heterochromia iridis.