A 6-year-old girl born to nonconsanguineous parents presented with abnormal patch of hair since 4 years. Her parents noticed circumscribed patch of curling and coiling of hair along with change in texture over the vertex of scalp. Birth and development history were normal. Family history was negative for such condition.\nOn examination, there was solitary cicrcumscribed patch of size 5 cm × 6 cm over vertex []. Hair over the patch had an altered texture, light in color, thinner, and tightly coiled. The hair in other areas of scalp was normal. Skin over the patch was normal. Linear epidermal nevus was present over the chin extending to the neck there [] was no evidence of palmoplantar keratoderma and precocious puberty. Based on the above findings, we arrived at a diagnosis of wooly hair nevus.\nLight microscopy of hair revealed irregularities of the cuticle and twisting of hair []. Dermoscopy revealed snake crawl appearance and knotting of hair []. Diagnosis of woolly hair nevus was made, and parents were counseled for benign nature of the condition.
We present a 3-year-old healthy girl, whose mother was concerned about recent hair changes. The patient had no personal or family history of cutaneous diseases. At physical exam, the girl had a phototype II skin, normal teeth and nails. The back of the scalp revealed a well-circumscribed patch of kinky, curly light blonde hair. The rest of the physical exam was normal. Dermoscopy was not performed at the time.\nWoolly hair nevus was diagnosed. The parents were counseled about the benign and chronic nature of this lesion. Ophthalmologic evaluation was recommended, but the parents of the patient refused. No further studies were performed [Figures and ].