A 10-year-old boy presented with multiple circumscribed patches of abnormal hair on scalp []. The first patch was noticed on vertex at the age of 7 years. This was followed by the development of three new patches during the last 1 year; two on both temporal areas and one on the occipital area. The hairs in the affected area were thicker, curlier, with random hair shaft orientation, and normal underlying scalp. Trichoscopy revealed abnormal kinking of hair shafts []. Varying diameters of a single hair shaft [], trichorrhexis nodosa-like features [], kinking, and damaged cuticle [], with normal pigmentation were observed on hair microscopy. Color of the affected hair shafts was dark and uniform. These characteristic features were absent on microscopy of normal surrounding hair shafts []. Histopathology showed abnormal bending of the hair follicle above the hair bulb [], and irregularities of inner root sheath near the bulb at the bending []. A detailed cutaneous and systemic examination along with cardiac, ophthalmic, dental, skeletal, and nervous systems evaluation did not reveal any gross abnormality.
A 6-year-old girl born to nonconsanguineous parents presented with abnormal patch of hair since 4 years. Her parents noticed circumscribed patch of curling and coiling of hair along with change in texture over the vertex of scalp. Birth and development history were normal. Family history was negative for such condition.\nOn examination, there was solitary cicrcumscribed patch of size 5 cm × 6 cm over vertex []. Hair over the patch had an altered texture, light in color, thinner, and tightly coiled. The hair in other areas of scalp was normal. Skin over the patch was normal. Linear epidermal nevus was present over the chin extending to the neck there [] was no evidence of palmoplantar keratoderma and precocious puberty. Based on the above findings, we arrived at a diagnosis of wooly hair nevus.\nLight microscopy of hair revealed irregularities of the cuticle and twisting of hair []. Dermoscopy revealed snake crawl appearance and knotting of hair []. Diagnosis of woolly hair nevus was made, and parents were counseled for benign nature of the condition.