A 10-year-old boy presented with multiple circumscribed patches of abnormal hair on scalp []. The first patch was noticed on vertex at the age of 7 years. This was followed by the development of three new patches during the last 1 year; two on both temporal areas and one on the occipital area. The hairs in the affected area were thicker, curlier, with random hair shaft orientation, and normal underlying scalp. Trichoscopy revealed abnormal kinking of hair shafts []. Varying diameters of a single hair shaft [], trichorrhexis nodosa-like features [], kinking, and damaged cuticle [], with normal pigmentation were observed on hair microscopy. Color of the affected hair shafts was dark and uniform. These characteristic features were absent on microscopy of normal surrounding hair shafts []. Histopathology showed abnormal bending of the hair follicle above the hair bulb [], and irregularities of inner root sheath near the bulb at the bending []. A detailed cutaneous and systemic examination along with cardiac, ophthalmic, dental, skeletal, and nervous systems evaluation did not reveal any gross abnormality.
A 5-year-old girl with a patch of kinky hair in the right parietal region, which had been present since the age of 4 months and different colored eyes since birth referred to our clinic []. The underlying scalp was normal. The affected hair appeared smaller in diameter and lighter than the normal hair color and no structural hair abnormalities were detected under the light microscope. She had slightly hyperpigmented linear lesions mostly marked on the anterolateral of the right arm with midline pectoral and abdominal extension []. The right eye was diffusely brown, and the left was green []. No ophthalmologic, cardiac, neurological or skeletal abnormalities were observed. Nails and teeth were normal. The patient was diagnosed with a woolly hair nevus of the right parietal scalp associated pigmented demarcation lines and heterochromia iridis.