A 5-year-old girl child presented with abnormal patch of hair since 2 years of age. Her parents noticed a single patch of curling and coiling of hair along with altered texture over the left side of scalp. Her parents felt the patch to be unruly and unsightly and hence attempted repeated tonsuring. In spite of this, the patch of hair remained the same. Birth and development history of the child was normal. Her family members did not have similar complaints. On examination, we noticed a solitary circumscribed patch of size 6×4 cm located over the left frontoparietal region of scalp. The hair over the patch had an altered texture, was lighter in color, thinner, tightly coiled, and curled giving an unkempt appearance []. The skin over the patch was apparently normal. Examination of rest of the scalp, teeth and nails were also normal. There was no evidence of palmoplantar keratoderma and evidence of any epidermal nevus elsewhere. Ophthalmic and cardiac evaluation did not reveal any abnormality. There was no evidence of precocious puberty. Based on the above findings, we arrived at a diagnosis of localized woolly hair nevus. Hair microscopic examination showed non-specific features. Scalp biopsy revealed normal hair follicles and appendages []. Routine hemogram, serum biochemistry, electrocardiogram and echocardiogram were normal.
A 6-year-old girl born to nonconsanguineous parents presented with abnormal patch of hair since 4 years. Her parents noticed circumscribed patch of curling and coiling of hair along with change in texture over the vertex of scalp. Birth and development history were normal. Family history was negative for such condition.\nOn examination, there was solitary cicrcumscribed patch of size 5 cm × 6 cm over vertex []. Hair over the patch had an altered texture, light in color, thinner, and tightly coiled. The hair in other areas of scalp was normal. Skin over the patch was normal. Linear epidermal nevus was present over the chin extending to the neck there [] was no evidence of palmoplantar keratoderma and precocious puberty. Based on the above findings, we arrived at a diagnosis of wooly hair nevus.\nLight microscopy of hair revealed irregularities of the cuticle and twisting of hair []. Dermoscopy revealed snake crawl appearance and knotting of hair []. Diagnosis of woolly hair nevus was made, and parents were counseled for benign nature of the condition.