A 7 month old girl presented with complaints of poor feeding, excessive crying and downgaze preference since 1 month. MRI [] showed a CSF-intensity cystic lesion of 7 × 5.7 × 5.8 cm size in left side of posterior fossa compressing the brainstem and cerebellar hemisphere to right with obstructive hydrocephalus and periventricular hyperintensities. The child underwent midline suboccipital craniotomy and decompression of cyst. On histopathology, the cyst wall was lined by pseudostratified ciliated cuboidal to flattened epithelium (black arrow) with a subepithelium composed of fibrocollagenous tissue with dilated vascular channels. On microscopic examination, the findings were suggestive of a neuroepithelial cyst, but based on the immunohistochemical properties, a final diagnosis of neuroenteric cyst was made.
A 17-year-old female patient presented with occasional headache since two years increased since the last three months. On examination, bilateral papilledema was present. No other focal neurological deficits were present.\nMRI [] showed a well-defined CSF-intensity cystic lesion in the region of the fourth ventricle with obstructive hydrocephalus. There were no enhancing solid components. The lesion showed facilitated diffusion. The patient underwent midline suboccipital craniotomy and deroofing of the cyst. Histopathology showed cuboidal or columnar epithelium (pseudostratified at some foci). Based on the immunohistochemical properties, a final diagnosis of neuroenteric cyst was made. Patient did well in the post-operative period with reduction of the hydrocephalus.