We report the case of a 27-year-old healthy male who presented with an area of curlier and thinner hair than the rest of his scalp localized on the right parietal area. He referred that just at that location, his hair had been different since childhood, curlier than the rest. Physical examination revealed a plaque with shorter and curlier hair on an area of 10 cm in diameter on the right parietal area of the scalp. A decreased density of hair was observed. The skin on the patch was apparently healthy. There were not exclamation mark hairs or miniaturization of hair follicles. A hair pull test was negative []. A skin biopsy showed a mild perifollicular lymphocytic infiltrate, telangiectatic capillaries in the superficial dermis and several terminal hair follicles emerged in the same dilated follicular infundibulum. Interestingly, an excessive amount of normal apocrine glands were found in the deep reticular dermis. Counting of hair follicles was normal [Figure –]. Based on clinical appearance and histopathologic studies, a diagnosis of WHN was established.
A 5-year-old girl with a patch of kinky hair in the right parietal region, which had been present since the age of 4 months and different colored eyes since birth referred to our clinic []. The underlying scalp was normal. The affected hair appeared smaller in diameter and lighter than the normal hair color and no structural hair abnormalities were detected under the light microscope. She had slightly hyperpigmented linear lesions mostly marked on the anterolateral of the right arm with midline pectoral and abdominal extension []. The right eye was diffusely brown, and the left was green []. No ophthalmologic, cardiac, neurological or skeletal abnormalities were observed. Nails and teeth were normal. The patient was diagnosed with a woolly hair nevus of the right parietal scalp associated pigmented demarcation lines and heterochromia iridis.