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SPILL THE BEER OF CHRIST!!!!
My art will be on display at Optic Nerve Arts in Portland, Oregon through June! This solo show collects 24 of my favorite drawings from the past few years and all original art will be available for purchase. I will also have affordable 16" X 20" digital prints of a few select works. Please come out and join us as we spill the beer...er...blood of Christ on 6/6/06. And tell your wimp friends to support REAL underground art!
Tuesday June 6th
7pm-Midnight
Optic Nerve Arts
1829 NE Alberta St.
Geometry of the Blood
The following is an abridged version of the interview with Robert Taylor that will soon appear in its entirety in issue #9 of Destroying Angels. Robert Taylor is one of the founders of contemporary Odinism in America. He is also the vocalist and founding member of late 60's folk band Changes, who are perhaps best remembered for their early association with the Process Church of the Final Judgement. A veritable Renaissance Man, Mr. Taylor is also an accomplished visual artist, poet, craftsman, and lyricist. The following interview was conducted in May 2006 and will appear in the upcoming issue of Destroying Angels, slated for release on Summer Solstice.
Dennis Dread: What does the word "heathen" mean to you?
Robert Taylor: In its literal meaning, it means simply a person of the heath (land or fields), a rural person subscribing to native folk religion and beliefs. It has the same meaning and connotation as the word "pagan" (countryman). I am sure in both cases it was a term of condemnation, sort of like the word "hillbilly" in America today. They all have illusions that are brought to mind when the word is said or made use of. In the current vernacular of today it implies more. It not only means a person who ascribes to and believes in the archaic natural deities of his folk or kind, but often is used to imply someone who has rejected the Christian faith and is in some way Anti-Christ or a heretic or devil worshipper. "Heathen" is often used to denote savagery and such. These other things are not accurate of course, but they are images created in the popular mind. Those of us who proudly assume the title of heathen see it as a sign of one's healthy mind, spirit and soul, and a return to primal sources of a primordial tradition. In essence, a return to one's true self as opposed to alien Salvationist faiths which promulgate a false sense of self.
Could you elaborate on your personal relationship with the Nordic/Germanic pantheon?
It has been a long (nearly 40-year) relationship on many levels, encompassing mystical experiences, scholarly study, much thought and deliberation and active participation in the rites and rituals of the path of Asatru. I was among the three people who more or less founded the Odinist/Asatru troth. The two other principle individuals were Elsa Christenson and Steven McNallen. We all more or less found the pathway to the Gods in the same several-year period. The differences in approach were that Elsa took a philosophic and less spiritual approach. Steve formed what was, in the beginning, a national organization of largely dispersed members with the original AFA (Asatru Free Assembly). My former wife (Karen) and I founded a locally based group of Asatru adherents and practitioners called the Northernway. Unlike Elsa's or Steve's approach we maintained the Northernway as a local group. That was because we did not want a mail order organization so much as a group of actual people who knew one another and conducted services and rites in person together. Eventually the AFA began to hold annual Althings and the group became more of a flesh and blood organization as opposed to simply subscribers to a publication and correspondents. Eventually, the Northernway broke into two groups: one essentially became a Norse or Germanic Wicca group (and after a couple of years went defunct) and those that came with us reformed into what became first the Wulfing Kindred and later, when we began to spread in numbers and geographic locations, the Tribe Of the Wulfings. At some point early on, we affiliated with the Asatru Free Assembly and became an active kindred of that organization, and remained so until it's demise. I view the Aesir and Desir from many points of view. As Jungian archetypes, as numinous forces of nature and the universe, as composite symbols of the Germanic and related people themselves. I also see them as pure spiritual entities and forces which guide their people from the inner planes. They are symbolic. They are metaphoric and they are actual in my personal experience, estimation and insights.
Stephen Flowers has shared his life-altering experience of hearing the word "Runa" whispered in his ear. Did you have an initiatory experience of this nature? Can you recall your first exposure to the Gods and Goddesses of Northern Europe?
My own introduction to Germanic spirituality was perhaps less prosaic and succinct then that of Dr. Flowers. I have had numerous mystical experiences over the years that partook both of the Germanic as well as the larger corpus of Indo-European symbology. One of those I covered in an article that was published in Robert Wards Fifth Path magazine titled 'Animal Spirit'. I'll not repeat that here due to its length and context. There is now a Robert Ward memorial website and perhaps one day articles from his Fifth Path magazine will be posted on the site for others to read. We all have dreams and many people have mystical experiences. The ones that matter most are those that give guidance which, when acted upon, have effects in the material world and in some way facilitate and further our spiritual quest. My introduction to the Germanic pantheon was by way of my own father, George Ellis Taylor, who considered himself a heathen all of his life and passed those thoughts and feelings on to me. Initially both Karen and I were among the very early people in the larger pan-pagan movement in the Midwest. We affiliated our Northernway group with the Midwest Pagan Conference, which held gatherings in and about the Midwest. We withdrew from the larger pagan community due to differing perspectives on just what paganism/heathenism really was and should be. We felt that the general pagan movement was too eclectic and contrived and lacked any real ethical code or basis. Much of it was based on the contrivances of people like Gerald Gardner, Alex Sanders and the largely British occultism of the early part of the 20th century Asatru, as it has evolved and as it actually was in its tribal period, was first and foremost a heroic/ethical religion. Theological concepts I think played an auxiliary part and were more the prerogative of the priest class (Gothis), Vitki (rune masters) and the exoteric side of Asatru. It largely remains as such in the present resurrection of Asatru overall. The primary ethics of Asatru can be found in the Havamal (Words of the High One).
You were among the very first to establish Asatru in America. Could you set the stage culturally for that period in the 70's? What was happening in your own life that helped guide you to Asatru?
I have answered the above question in part already. As for the cultural stage of things at the inception period of Asatru, life was in a general flux culturally and more importantly in a spiritual sense. Early on, perhaps as early as 14 years old, I began to be aware of this spiritual crisis. In the larger European context, this crisis begins with the German philosopher, Fredrich Nietzsche. Even before Nietzsche, one can find the seeds of it in Schopanhauer and Hegel, but it comes into full focus and expression in the writings of Nietzsche. In a sense all roads lead back to Nietzsche and begin with him as far as this spiritual crisis is concerned. I can hardly imagine anyone having a grasp of this crisis, both spiritual and intellectual, without studying his writings. I derived immense insight from studying his thoughts in relation to all of this. If I recall correctly, it was in my fourteenth summer that I began studying his works at the suggestion of my father. I spent nearly an entire summer reading his collected writings in English translation at the main downtown library in Chicago. This was followed by reading and studying the works of Oswald Spengler (particularly his Decline of the West) and Houston Stewart Chamberlain's Foundations of the 20th Century, and Egon Friedel's A Cultural History of the Modern World -all of which drew similar conclusions in their own manner, and all of which owed a huge debt to the philosophy of Nietzsche. Having studied, analyzed and pondered on these works, the question that remained was, how can we reverse the downward spiral of Western civilization? A spiritual rebirth seemed necessary to affect this decline. Christianity had become so played out and corrupted of spirituality that it did not seem the answer in any way whatsoever. It was already dying or dead. It was in a large part the religion that was at the forefront of the decay and decline. Nietzsche had already dissected it to its marrow, but what could take its place? A return to an honest spirituality was the general answer I came to. The Eastern religions are in many ways as corrupted as Christianity is. Plus, like Christianity, they are alien to the true nature of Western man and the Western soul. They are all constructs or expressions of other people, not us. I could find no real resonance in any of them myself. Buddhism is an ethical philosophy of passive nihilism. Nietsche's nihilism is its anti-thesis. It extols heroic active nihilism, but the Arlen Specter of nihilism or the teetering edge of the abyss is not an answer in and of itself. It is largely a diagnosis of things. Cultural Pathology 101. As Tony Wakeford's song 'Looking for Europe' says, "If you're looking for Europe just look in your heart." Or as the Changes song says in a slightly different variant, "For the soul to know the soul, to the soul you first must go, for the answers lie there hidden in the legends that we know."
I felt it was necessary to return to our own spiritual roots and build up from there, and I spent the next two decades finding the soul of Western man. I found it in what later emerged as Asatru. It was and is the answer. We as Western people must draw from within ourselves, from within the true Western legacy of our legends and myths and archaic beginnings, and it does not simply end there. We must take what we have found and re-seed it with a new vision, a new creativity, a new and vibrant spirit.
What was your role in the Minutemen movement? Were you arming yourself for the impending collapse of American society?
I began association with the Minutemen in my early teens. As I grew older, so did my involvement develop from member to local leader, to executive council as head of the organization's intelligence, and finally as National spokesman for the group and publisher of the organization's publication, On Target. We were arming and training for the Second American Revolution. I know it is a given that when you mention the Minutemen, the first thing that comes to most people's minds is guns. In actuality, guns played a much lesser role than intelligence, counter-intelligence psych-war, and such things as those. Though ostensibly an armed citizenry preparing against the threat of international communism on the surface, the true aims of the organization were revolutionary. The revolution had as its goal the reestablishment of America as a constitutional republic replete with the checks and balances it had been founded upon. We felt our liberties were being legislated out from under us all, and they were. Most of the warnings on these things have come to pass as it were. Most of the freedoms and liberties we have on the books are more apparent than they are actual. Try using them and you will quickly realize that you are under surveillance by the secret police. That is what occurs as soon as you elect to exercise such guaranteed liberties. Our leaders offer license in place of these actual liberties. They will persecute anyone using the first amendment rights in an adversarial manner toward them, but they will allow you the license of watching women get it on with barnyard animals on the internet. Our world today is full of license and deficient on true liberty. It is a very bad trade-off.
Have you received much attention from the FBI since those days?
Yes, to be sure--undo attention by them or the other intelligence agencies that have no mandate to operate domestically. They investigated and interviewed family, friends, neighbors, etc. I had my phone taped, mail covers, agent provocateurs and such which they utilized in one manner or another. I'm sure I've kept a lot of agents busy and working and earning their salaries for decades. Even now, I am listed on the immigration security list as some sort of dangerous character and put through the usual indignities every time I travel by air. And in the nearly forty years they have been giving me attention, nothing practical has evolved from their standpoint. You would think, after that much time, they would wise up and allocate their efforts elsewhere, where it might do them some good or serve some actual advantage. Maybe they missed 9-11 so completely because they were all preoccupied with shadowing people like myself who have done nothing they can construe as illegal. After forty years, you would think they would find something more profitable to allocate their resources toward. One thing I have come to think after all the years of their attention is that they are very myopic of mind and there isn't a great deal of real imagination among these types of people. suppose one can justifiably expect too much of accounting and pre-law students. They are hardly the epicenter of imagination or very profound thoughts. Interestingly, as I write this, there is a big flap over telephone taping or surveillance by the Bush oligarchy in Washington. It seems like most all of what I have predicted over the years is coming to fruition. And I don't think Specter is going to save the nation from further tyranny. Only the American people as a whole can possibly do that. I can't imagine what they're all waiting for. A leader?
Would you agree that your visual works, similar to mandalas, reflect a yearning for wholeness?
That is the general thesis, that such round art is an attempt to reach or acquire wholeness of being. I started doing mandalic-type art in the late sixties. There was nothing in particular that inspired me to do so. I had no real knowledge at the time about oriental art or religion or Jung's writings. I was quite amazed when I first encountered other artists who were in effect doing similar mandalic art like that which I was doing in the late sixties. I instinctively thought that there must be a deeper reason for this synchronistic occurrence in art. I am sure it was as you mentioned a desire toward wholeness, as Jung would imply. The modern world is a very fragmented wasteland. That fragmentation is within us as people (a spiritual crisis) as well as on the temporal material level around us (environment). I saw zietgeist in the art of that period being projected in such work. There also was the prolific use of psychoactive plants and drugs which created a shared experience among a large number of people who did not necessarily even know of one another. This in itself was, I am certain, another factor in the rise of such in approach as mandalic art. I did drawings and paintings as well as shaped verse (concrete poetry; calligrams; pattern poems) also in a mandalic mode. In fact, I had a one-man exhibit in Chicago of my mandalic art and calligraphic devices. I titled the show Full Circle: Art and Poems in the Mandalic Modeâ. Today when I do anything in what could be termed the mandalic modeâ it is simply one of the ways I create and express something. I am no longer seeking totality of being or wholeness. I think I largely achieved that long ago. I have pretty much gone through the individuation process of life.
What effect would you like your visual work to have on the viewer?
A visual effect. I consider myself an op-artist and love to employ the optical in the visual art I do. I have explored, and continue to explore, ways of using optics in my art: hidden pictures, anamorphic distortions, optical illusion, geometric impossibilities alluding to a fourth dimension, chroma-depth techniques, 3-D, subliminal and other similar approaches and meldings of such. I love to play with the human optical apparatus and mind. To surprise; to transfix; to perplex. I am a bit dismayed that there are practically no real books concerning op-art that I am aware of. Plenty on pop art and every other type of art, but little relating to op. There are some books on optical illusion art, or books on actual optical illusion techniques, but nothing in print that I know of which covers the movement of op-art. I think there is a corollary between op-art and what is termed fantastic or fabuklist literature in the vein of Jorge Louis Borges, Danilo Kis, Italo Calvino, Milorad Pavic and others. I am not in any way the first artist to do optically oriented art. You will find many such optical gambits in the work of DaVinci, Durer and artists of every period and time. Dali in our own time used such devices and ploys in many of his works, as did Dutch graphic artist Escher. Especially Escher and his disciples such as Sandro. A prime similitude that artists who have done so seem to share is a knowledge and practical ability in the realm of geometry. It is a given of sorts toward crafting such art. About fifteen years ago, I came upon the subject of geometry. It all began with a project I was getting together at the time. I had a 14-foot reinforced concrete slab laid in the middle of a field on the farm I had at the time. My intention was to build an astronomical dome that would sit upon the slab. One of the ideas I had was to paint a mural time-line of the history of astronomy. To do so, I would need to know how many linear feet of painting I would require to complete the painting on the wall from one side of the door to the other. That, of course, required the pi equation. I never finished the dome and hence never did the painting except a few preliminary sketches. The same day I was figuring out the pi ratio for that project, I happened upon two people whom I knew at a local restaurant discussing pi ratios and there were other synchronicities that occurred that day on such sacred geometry. I had a volume containing both the books and propositions of Archimedes and Euclid. I spent the rest of that winter studying the propositions and working them out on paper. So I acquired something of a crash course in geometry. Since that time, geometry has become an integral part of my daily life, perhaps as much as poetry is. I am sure I am not through with it yet. Several times I thought I had gone about as far as I could with it, and then some new insight occurred and I was off and running on it again. Geometry is a very old practice, an archaic subject. There is not a lot that one can add to it today (at so distant a time from its inception). Many great minds have wrestled with the subject and added some small contribution. DaVinci was a very able geometer. His melding of the icosahedron and the dodecahedron into what is called the icosidodecahedron, which has 20 triangular faces and twelve pentagonal faces, was certainly a stroke of genius. Durer was an even more knowledgeable geometer than was DaVinci. Geometry for the artist is a challenge as to how one might employ geometric knowledge and skill in representational art. Escher was a master at this. He was able to take geometry and turn it into graphic art of a high level. His concepts and skills have always left me awed. I am still grappling with the matter of employing geometric knowledge in a representational manner. Most of my artistic efforts of the past several years have been devoted to doing that. Two of the three contributions I had in the recent Heathen Art show were eggs done with design and geometry. I think the initial inspiration for doing egg-shaped art was as a result of having investigated the visica pisces. The visica pisces is the center shape created by overlapping two circles. The curved lines of the inner arc of the circles cross at the center of one another forming what is termed a mandala at the center. It is very much similar to an egg shape; in fact, an egg shape can be created from the visica pisces, as can all the archimedian and platonic solids be created within the shape. It is termed by the classical Greeks as the womb of geometry or the womb of numbers.
Several years ago you described your construction of the Wulfing hof as "the pinnacle of my personal creative endeavors." Do you still feel this way? What has become of the hof now that you've moved?
I did think so at that time. I think the Opus Dei project will transcend that project in a quantum way, though the hof project was a worthwhile one in so many ways. Most unfortunate was the fact that it was never totally completed. There was much carving and decor to be added both within the hof as well as without. It was completed in the sense of a structure and was closed in, had a roof, windows, doors, etc. I did some of the decor on the inside--mostly the wide baseboards that undulated like a serpent. I also completed a world tree and other runic devices within. The Dragon's Head montage I had in the Heathen art show was a design for a dragon's head to be fashioned of wood and installed in the hof. I also have designs for the dragon's wings and tail which I may one day do as a similar paper montage. All three of these things were to grow out of or emerge from the undulating baseboard on either side of the Irmunsil Tree. It is no longer being used as a hof as far as I know. Initially, there was an agreement with my ex-wife that the hof would be set aside for Asatruars and maintained from a joint trust fund set up to pay the taxes on it, but that agreement never materialized. It was just one of many promises and agreements that were broken. Such is divorce and the parting of ways with human beings.
Do you have a less elaborate hof or similar "sacred space" for spiritual activities at your current home?
I do have plans of building another hof at sometime in the future. I have other projects I am concerned with at the moment. I think it will be very different from the previous one in the way I design and build it next time. I had an area set aside for that in my home until recently. I remarried this summer and am presently in the process of renovations and reorganization of my house. Once I have squared the main of that away, I will find an area to once again set up a sacred space or shrine.
If you could change any aspect of modern society right now, what would you change?
The people within it. Make them self-reliant and not dependent on powers outside themselves. Expand individual liberties while at the same time generating through all medias and education the responsibilities necessary in maintaining said liberties. Only responsible people can maintain any measure of liberty and selfhood as individuals.
How might your art (visual, writing, music, etc.) assist toward this aim?
In continuing to respond to interviews like this one and helping to clarify issues and reinstating sound principles that safeguard our individual lives and fortunes as a people.
The Changes song 'Twilight of the West' is perhaps your most challenging political statement in that you articulately address much of your frustration with modern society. Could you explain what a more ideal contemporary society might look like?
A traditional society would be best, if it were imperative, due to population numbers and the complexities of a technological society. If those considerations were absent, then I would personally prefer to live in a Free State system, much like our American West was before civilization and its expanded population caught up with it. A similar free state system existed in Iceland in its early years. Of all American statesmen, Thomas Jefferson is my favorite social philosopher and governmental architect. It was Jefferson who said, "The government is best which governs least of all." Thoreau of course one-upped Jefferson with his paraphrase, "The government is best which governs not at all." I think, however, that Thoreau took it a bit too far. I believe in law and justice. Without some form of fair and equitable law and justice, we end up with the sort of criminal outbursts recently exhibited by some of the residents of New Orleans in the wake of disaster and a cessation of law enforcement. Anarchy always ends up as thugism and an open invitation to criminal elements in a society to have a field day of rape, robbery and destruction as was witnessed in New Orleans. As for 'Twilight Of The West' I think it continues to be fulfilled in its import and meaning. Perhaps that's why my adversaries seem to hate it most of all. It sort of rips the mask off things, on both the inner and outer plane, that are currently unfolding. As much as I hate to quote my own poetry, I feel impelled with the thought: See? I told you so! "And opponents you thought vanquished have come to take their fill as they hover on the sidelines preparing for the kill." I think I summed up something of the current controversy of the 11 million ingratiating illegal aliens that have poured mostly unchecked across our southern border and are now demonstrating in our midst. Some of them, like the head of the Azatlan movement in the southwest, are saying that it may be necessary to start killing old white people before they get what they want. And what do they want? To take back Texas and the southwest and other areas once a part of Mexico. I foresee many little Alamos occurring in those areas in the future. And like the demonstrated reluctance of the federal government to do anything about the illegal flow into the U.S., they will, I am certain, leave all the Americans in those areas in the lurch to be slaughtered if that begins to occur. That was exactly what I was thinking of in 1973 when I wrote that while residing in New Mexico. We surely do live in interesting times and I'm sure it will get more interesting in time.
The Red Salon
My copies of the new Autopsy DVD arrived today from England. They look pretty nice, although the folks at Peaceville conveniently cropped my name out of the cover artwork and plastered the band logo across one of my favorite parts of the drawing. This is especially frustrating because I drew the art to accomodate the text and Peaceville was initially very professional about requesting my layout approval. But I won't complain too much because I have to admit that I'm still extremely pleased to have my art on an Autopsy DVD! Well, that and I've grown accustomed to this sort of thing over the years. I'm also not too worried because I'll soon have really nice looking 16" X 20" prints of the cover art available without any text!
As for the DVD itself, it's pretty much a no-frills homemade documentary capturing some awesome shows by this great legend of death metal. Kind of like 'Cliff 'Em All' but with more bongs and much more shaving cream. If you're a hapless poser who missed out when they toured the states in the early 90's (like me) then this is about as close as you'll ever get to the live Autopsy experience. The band sounds great and they bash out a killer collection of favorites. The one thing missing that I really hoped to see is the gory homemade video that the band recorded early on. Instead we get a 'Gummo' moment with the band rehearsing and smoking a joint in some house with little kids running around behind the amps.
I spoke to Chris Reifert last week and he told me that, in the end, about half the material didn't make it onto these discs. Which means there are still several unreleased Autopsy shows! I'm crossing my fingers that there might be a Part 2 or "deluxe edition" at some point. Anyway, I'll have a few copies of the DVD for sale at my upcoming show at Optic Nerve Arts on 6/6/06. I'll also be displaying the original art. Maybe I'll set up a TV and just have a mini screening.
Posted by Dennis Dread at 1:05 AM 0 comments


Leading global contractor Multiplex has reached a major construction milestone on M&L Hospitality's new boutique hotel at 65 Sussex Street in Sydney's CBD, topping out the eight level building.
Designed by architects Fitzpatrick + Partners with interiors by Wood Bagot, the hotel will feature a distinctive geometric façade and comprise 182 guest rooms including four generously-sized suites, a three storey high internal garden and courtyard, meeting space, restaurant and bar.
According to Multiplex, the construction of 65 Sussex Street has seen over 550 people and 85,000 hours worked on-site to date. Almost 3,000 cubic metres of concrete has been used to build the hotel's structure, while 333 individual panels of glass will be used to form the geometric façade.
"The hotel is an important part of the revitalisation of the surrounding western corridor and is ideally located close to the Barangaroo and King Street Wharf lifestyle precincts. We are drawing on our expertise in hotel construction and working within the confined and busy CBD environment to deliver this new hotel," said Mr David Ghannoum, Regional Managing Director NSW at Multiplex.
"We are excited to reach this important milestone and look forward to launching our new boutique hotel later in 2017." Said Mr Neil Maxwell, CEO of M&L Hospitality.
With the structure of 65 Sussex Street complete, Multiplex will now commence the internal fit-out of the guest rooms with completion on track for the end of 2017.
In December, 2016 Multiplex completed the redevelopment of M&L Hospitality's 161 Sussex Street property at Darling Harbour with the hotel opening as Hyatt Regency, representing the iconic hotel brand's return to the Sydney market.
The 161 Sussex Street redevelopment project saw the refurbishment of the existing hotel; the construction of a new 3,667 square metre convention centre; and a 25-level tower including 13 new hotel levels and 10 levels of A-grade high rise commercial office space.


I've never been brilliant with money. Growing up, Thursday nights were a night of dread and fear. My dad got his wages on a Thursday. In the 1980s in industrial Sheffield the wage packet was something to be both revered and dreaded. Amazing that such a tiny double folded piece of brown paper could wield such power. Inside, neatly folded, would be my dad's pay for the week, in cash. It always looked like a fortune. After tea (always plenty of bread and butter, which I now realise was there to fill us up when the meat wouldn't stretch) my dad and mum would clear the table and then sit back down and open the wage packet. I remember vividly my dad counting out the notes into little piles: the gas, the electric, the money for the insurance man and then a small pile pushed over to my mum 'for housekeeping'. Most of the time it was enough. When Dad was made redundant one Christmas Eve, Mum took on three jobs so we could manage and my brother and I had to have free school meals. Money was a thing to be feared and revered in our house.
All this sent my brother and I separate ways when it comes to our attitude to money. My brother went on to become a sales person, flogging anything and everything he could. Working his way up, he now drives a very big car and lives in a very big house with a very small family. He's very happy and very well off. I, on the other hand, want nothing to do with money. When Graham and I tried to buy our first house when I was 23, the mortgage provider asked me for three months' worth of bank statements. I didn't have any. I never opened them and threw them straight in the bin. Even now, with two degrees and a responsible job, a community leader, I still won't phone the bank and if we have to go into the branch I stand outside while Graham deals with it all.
Being a vicar of three churches is essentially like running three small businesses and in two of my three money is a real worry. I didn't give anything financially to the church when I first came to faith. I was a teenager and when I suggested to my dad I might like to give some of my pocket money to the building project at my church he said 'I'll tell you this - the Church of England is one of the richest land owners in this country and they stole some of that land. The churches are full of gold and silver and yet they ask the people for money? Don't be a fool.' When I got married to a vicar's son who'd grown up tithing there was a clash of cultures.
Preaching on the subject of money is my least favourite thing. A clergy colleague of mine hates it so much that he always drafts in a vicar from another patch. I've taken my three churches through giving campaigns in the last five years and the subject does not come easily. I recently preached on tithing. Being from good evangelical stock this has always been a teaching I thought was standard. Not so. One congregation member in his 80s, formerly of Eton and Trinity, Cambridge and a lifelong daily worshipper, grabbed me afterwards and told me he's never heard of such an idea and was I absolutely sure there was some biblical evidence for it.
When I preach on money I tend to tell the story of what changed for me when I went from being someone who didn't give to someone who did give to the church. I knew the money wasn't really mine 'and of your own do we give you', I knew that the church needed it as they were 'asset rich yet cash poor' but what changed for me was that I started to see that giving was part of my worship. And when I heard my father in law (to be) describe the act of giving money as an act of worship itself, that's when it changed. No longer did this seem a functional exercise aimed at repairing the roof or a crumbling bell tower, this became about my relationship with God. In that sermon he talked about not the amount but the attitude being key to being a cheerful and generous giver and that if I was to give grumpily and reluctantly then I could keep my money.
Kate Bottley is an Anglican priest, wife and mother, who stars in Channel 4's Gogglebox. She gained a national profile when a YouTube video of her leading a flash mob at the end of a wedding ceremony went viral in 2013, and has since done a wonderful job of dismantling stereotypes about Church of England clergy.


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Vol 8 (2016): Review, Original Articles, Case Reports
THE ICET-A SURVEY ON CURRENT CRITERIA USED BY CLINICIANS FOR THE ASSESSMENT OF CENTRAL ADRENAL INSUFFICIENCY IN THALASSEMIA: ANALYSIS OF RESULTS AND RECOMMENDATIONS
Thalassemia, adrenal insufficiency, pitfall in the diagnosis, ACTH stimulation test, guidelines.
De Sanctis, V. (2016). THE ICET-A SURVEY ON CURRENT CRITERIA USED BY CLINICIANS FOR THE ASSESSMENT OF CENTRAL ADRENAL INSUFFICIENCY IN THALASSEMIA: ANALYSIS OF RESULTS AND RECOMMENDATIONS. Mediterranean Journal of Hematology and Infectious Diseases, 8, e2016034. https://doi.org/10.4084/mjhid.2016.034
Vincenzo De Sanctis *
Affiliation not present.
Vincenzo De Sanctis | vdesanctis@libero.it
Introduction: In March 2015, the International Network of Clinicians for Endocrinopathies in Thalassemia and Adolescent Medicine (ICET-A) implemented a two-step survey on central adrenal insufficiency (CAI) assessment in TM patients and after analysis of the collected data, recommendations for the assessment of hypothalamic-pituitary- adrenal (HPA) axis in clinical practice were defined.
Methods: To ascertain the current practice for assessment of CAI in thalassemia, the Coordinator of ICET-A sent two questionnaires by email: i) The first to evaluate the current interpretation of basal serum cortisol level (first step) and ii) The second to evaluate the current usage of ACTH test and the variability in practice" (second step). Based on the surveys the core ICET-A group prepared the recommendations for the assessment of suspected CAI in thalassemia (third step).
Results: A total of 19 thalassemologists/endocrinologists have participated in the first survey and 35 specialists participated in the second step questionnaire. The survey demonstrated a considerable variability in almost all aspects of relevant current criteria used for the diagnosis of CAI. A ROC analysis using peak value > 20 μg/dl (> 550 nmol/L), after ACTH stimulation test, was performed with the aim of identifying the optimal basal serum cortisol cut-off. The optimal threshold that maximizes sensitivity plus specificity for morning basal cortisol against peak post-ACTH value >20 μg/dl (>550 nmol/L) was 10 μg/dl (275 nmol/L).,Furthermore, the values associated with highest negative predictive value (NPV) and highest, positive predictive value (PPV) were 4.20 (115 nmol/L) and 18.45 μg/dl (510 nmol/L), respectively.
Surprisingly, 20 specialists in thalassemia working in blood bank, thalassemia centres (day hospital), internal medicine, hematology and onco-hematology had poor knowledge and experience in testing for CAI and stopped filling the questionnaire after the second question. In contrast, 9 endocrinologists (8 pediatricians) and 6 hematologists working in collaboration with endocrinologists completed the questionnaire.
Conclusions: While waiting more extensive adequately powered and targeted studies, physicians should adopt an acceptable policy for accurate assessment of HPA in TM patients. Regular surveillance, early diagnosis, treatment and follow-up in a multi-disciplinary specialized setting are also recommended. The ICET-A recommendations are reported in order to facilitate for interested physicians the approach to successful assessment of adrenal function in thalassemia.
Key words: Thalassemia, adrenal insufficiency, pitfall in the diagnosis, ACTH stimulation test, guidelines.
Vincenzo De Sanctis, Ashraf T Soliman, Giancarlo Candini, Christos Kattamis, Giuseppe Raiola, Heba Elsedfy, Liver iron concentration and liver impairment in relation to serum IGF-1 levels in thalassaemia major patients: A retrospective study , Mediterranean Journal of Hematology and Infectious Diseases: Vol 7 (2015): Review Series, Original Articles, Case Reports
Vincenzo De Sanctis, DOES INSULIN LIKE GROWTH FACTOR-1 (IGF-1) DEFICIENCY HAVE A "PROTECTIVE" ROLE IN THE DEVELOPMENT OF DIABETIC RETINOPATHY IN THALASSEMIA MAJOR PATIENTS? , Mediterranean Journal of Hematology and Infectious Diseases: Vol 7 (2015): Review Series, Original Articles, Case Reports
Vincenzo De Sanctis, Late-onset male hypogonadism and fertility potential in thalassemia major patients: Two emerging issues , Mediterranean Journal of Hematology and Infectious Diseases: Vol 7 (2015): Review Series, Original Articles, Case Reports
Vincenzo De Sanctis, ACQUIRED HYPOGONADOTROPIC HYPOGONADISM (AHH) IN THALASSAEMIA MAJOR PATIENTS: AN UNDERDIAGNOSED CONDITION? , Mediterranean Journal of Hematology and Infectious Diseases: Vol 8 (2016): Review, Original Articles, Case Reports
Vincenzo De Sanctis, Heba Elsedfy, Ashraf T Soliman, The diagnostic approach to central adrenocortical insufficiency (CAI) in thalassemia , Mediterranean Journal of Hematology and Infectious Diseases: Vol 8 (2016): Review, Original Articles, Case Reports
Vincenzo De Sanctis, THE ICET-A RECOMMENDATIONS FOR THE DIAGNOSIS AND MANAGEMENT OF DISTURBANCES OF GLUCOSE HOMEOSTASIS IN THALASSEMIA MAJOR PATIENTS , Mediterranean Journal of Hematology and Infectious Diseases: Vol 8 (2016): Review, Original Articles, Case Reports
Vincenzo De Sanctis, REVIEW AND RECOMMENDATIONS ON MANAGEMENT OF ADULT FEMALE THALASSEMIA PATIEΝTS WITH HYPOGONADISM BASED ON LITERATURE REVIEW AND EXPERIENCE OF ICET-A NETWORK SPECIALISTS , Mediterranean Journal of Hematology and Infectious Diseases: Vol 9 No 1 (2017): Review, Original Articles, Case Reports
Vincenzo De Sanctis, A Young Adult with Unintentional Acute Parenteral Iron intoxication Treated with Oral Chelation: The Use of Liver Ferriscan. , Mediterranean Journal of Hematology and Infectious Diseases: Vol 9 No 1 (2017): Review, Original Articles, Case Reports

redpajama_set_name: RedPajamaCommonCrawl


The other day, a friend of mine and I watched Hedda Gabler, which is a play by the Norwegian playwright Henrik Ibsen. I haven't been to the theatre recently, so I was quite looking forward about this.
I have to say, I knew nothing about this play. It was just a spontaneous decision to watch it. We didn't even have tickets before, we just headed to the theatre hoping that there were still tickets for that evening. It turned out there was, and so we were able to watch it.
So, Hedda Gabler is a psychological thriller about emotional manipulation and personal freedom. The main character happens to be a female, who, during the time this was written, females were rather subdued and second-class compared to males. Hedda Gabler is rather modern for her society: she doesn't like to be relegated into the background, and therefore she decides to manipulate the people around her. However, this brings drastic effects.
I loved the way that there wasn't a main character that is easily likeable in the story. Every major character had a flaw of some sort, whether it is alcoholism, geekiness, or just a propensity for manipulating other people. Evil was oozing out of every person in the story, and it was just quite a treat to watch.
I also liked the production of this play. The play was directed by Kevin Leary, a graduate student. The costumes were perfect, and I liked that the costumes by Hedda Gabler contrasted quite well with the costumes of the rest of the cast. The lighting and stage set was also rather appropriate. As much as this is a student production, I have always been impressed with their productions, that I make it a point to attend every production.
So yes, after watching this play, I was glad I did. I haven't been familiar with the works of Henrik Ibsen at all, but watching this made me curious about his other works.


for the Body, Mind, Spirit & Soul.
Movement, Shamanic Healing, and Creativity.
Movement, in Cree, waskawewin, defines life. When somebody dies they stop moving, aponwaskawecik. If you asked "What is life?", a simple explanation using the Cree language would be that life is movement.


The services are also very important in ensuring that the safe that he or she used is completely locked by the fingerprint scanning so that no other person can be assured that no other person can be able to access the place where the safe is locked in. This is very important in preventing people from stealing properties from others that are living in the same vicinity. The article is going to focus on the importance of the finger print services to the many individuals that are surrounding it. It is something that is particularly important.
The first thing that we can be able to know is that, the finger printing services are very important in the whole idea of taming the crime. This is because, in any crime scene, the police must be able to dust for the finger prints so that they can be able to know the exact people that were in that given crime scene fingerprinting children. This is something that many people are able to do and they can only succeed in doing this if they are accurate and have the records of the country's population. We cannot be able to do this if we do not have the required things to deal with the continued rise in the country's crime rate. It is something that many people even in many countries do so that they can be able to protect the citizens.
It is important so that we can have the doors that are automatically locked by the use of these Fingerprinting Express. This is something that is very important to any given persona even the company in general. This is because, the doors that are locked by the use of the finger prints can only be here with us and no one can be able to force some of the entry into the building if he or she is not given the license to do this as nevada notary application. This is something that we should be able to admit and even implement as you can read more now.


text:
Q: RC522 board not working, red led is on I have a RFID RC522 board that was working perfectly, until by mistake I tried to write it with a phone as if it was a RFID tag and now it stopped working, in the way that its led still turns on but it's not recognised by the code (it says firmware version 0x0).
I guess writing it fried the chip, but is there any way to check if it's actually fried or just a software problem?

A: Because MFRC522 does not support Card emulation mode, When you put both PCD chips in writer mode across each other(Phone and RC522), generated field by the phone may damaged the RC522, but any way there is a version register in MFRC522 chip, try to read this register,if it was not returned successfully,means your rc522 is damaged.

redpajama_set_name: RedPajamaStackExchange


The first time that architect Robert Tretsch visited the luxury high-rise condo-hotel that is now the Waldorf Astoria Atlanta Buckhead, he rode a buck hoist and climbed several ladders to reach the top stories that were under construction. That was in 2006, when Harrison Design was asked to create the first model condominium for the 42-story tower's private residences, which was finished in 2007.
About four years later, the owners invited the firm back to devise a more modern look for the condos. When the model unit was completed, it sold almost immediately. With that auspicious new start, HD's Modern Studio took the lead in designing the property's two- and three-bedroom apartments. In eight years, the team has designed and completed 37 high-rise residences in 26 stories, as well as two penthouses. Seventeen floors feature two apartments per story, while nine floors offer full-floor layouts. All the apartments offer stunning views of the Atlanta environs and quality finishes and amenities appropriate for one of the city's most luxurious destinations.
A dramatic rhythmic arcade features classical underpinnings (left photo: Mali Azima); the tower was designed by Robert A.M. Stern Architects (right).
The work is still not quite complete, as the architects are currently finishing three townhouses in the rear of the site. In the 12 years, three hospitality groups—Rosewood, Mandarin Oriental and Waldorf Astoria—have managed the hotel, while Harrison Design has held steadfast.


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Literature Quotes
Authors: A B C D E F G H I J K L M N O P Q R S T U V W X Y Z
Categories: A B C D E F G H I J K L M N O P Q R S T U V W X Y Z
Go to Gemtracks Beats
South African literature is a literature in bondage. It is a less-than-fully-human literature. It is exactly the kind of literature you would expect people to write from prison.
south-african-literature-is-literature-in-bondage-it-is-less-than-fully-human-literature-it-is-exactly-kind-literature-you-would-expect-people-to-write-from-prison
Unknown Author Quotes
Literature must become party literature. Down with unpartisan litterateurs! Down with the superman of literature! Literature must become a part of the general cause of the proletariat.
literature-must-become-party-literature-down-with-unpartisan-litterateurs-down-with-superman-literature-literature-must-become-part-general-cause-vladimir-lenin
Literature cannot develop between the categories "permitted""""not permitted""""this you can and that you can't." Literature that is not the air of its contemporary society, that dares not warn in time against threatening moral and social dangers, such literature does not deserve the name of literature; it is only a facade. Such literature loses the confidence of its own people, and its published works are used as waste paper instead of being read. -Letter to the Fourth National Congress of Soviet Writers
literature-cannot-develop-between-categories-permittednot-permittedthis-you-can-that-you-cant-literature-that-is-not-air-its-contemporary-society-aleksandr-solzhenitsyn
Christ and the life of Christ is at this moment inspiring the literature of the world as never before, and raising it up a witness against waste and want and war. It may confess Him, as in Tolstoi's work it does, or it may deny Him, but it cannot exclude Him; and in the degree that it ignores His spirit, modern literature is artistically inferior. In other words, all good literature is now Christmas literature.
christ-life-christ-is-at-this-moment-inspiring-literature-world-as-never-before-raising-it-up-witness-against-waste-want-war-it-may-confess-william-dean-howells
Nothing is harmful to literature except censorship, and that almost never stops literature going where it wants to go either, because literature has a way of surpassing everything that blocks it and growing stronger for the exercise.
nothing-is-harmful-to-literature-except-censorship-that-almost-never-stops-literature-going-where-it-wants-to-go-either-because-literature-has-way-ali-smith
I think it can be tremendously refreshing if a creator of literature has something on his mind other than the history of literature so far. Literature should not disappear up its own asshole, so to speak.
i-think-it-can-be-tremendously-refreshing-if-creator-literature-has-something-on-his-mind-other-than-history-literature-far-literature-should-not-disappear-up-its-own-asshole-to-
I looked into the literature on this, " said Nightingale, "and it wasn't very helpful." "There's a literature about this?" "You'd be amazed, Constable, about what there's a literature on.
i-looked-into-literature-on-this-said-nightingale-it-wasnt-helpful-theres-literature-about-this-youd-be-amazed-constable-about-what-theres-literature-on-ben-aaronovitch
Given the devaluation of literature and of the study of foreign languages per se in the United States, as well as the preponderance of theory over text in graduate literature studies, creative writing programs keep literature courses populated.
given-devaluation-literature-study-foreign-languages-per-se-in-united-states-as-well-as-preponderance-theory-over-text-in-graduate-literature-marilyn-hacker
Most British playwrights of my generation, as well as younger folks, apparently feel somewhat obliged to Russian literature - and not only those writing for theatres. Russian literature is part of the basic background knowledge for any writer. So there is nothing exceptional in the interest I had towards Russian literature and theatre. Frankly, I couldn't image what a culture would be like without sympathy towards Russian literature and Russia, whether we'd be talking about drama or Djagilev.
most-british-playwrights-my-generation-as-well-as-younger-folks-apparently-feel-somewhat-obliged-to-russian-literature-not-only-those-writing-for-tom-stoppard
Human beings don't necessarily exist inside of (or correspond to) the neat racial, gendered or national boxes into which we often unthinkingly place them. It's a mistake to ask literature to reinforce such structures. Literature tends to crack them. Literature is where we free ourselves.
human-beings-dont-necessarily-exist-inside-correspond-to-neat-racial-gendered-national-boxes-into-which-we-often-unthinkingly-place-them-its-mistake-to-ask-literature-to-reinforc
The body of literature, with its limits and edges, exists outside some people and inside others. Only after the writer lets literature shape her can she perhaps shape literature.
Annie Dillard
the-body-literature-with-its-limits-edges-exists-outside-some-people-inside-others-only-after-writer-lets-literature-shape-her-can-she-perhaps-annie-dillard
I love the Russian classics very much, the Russian classical literature. But I also read modern literature. As far as Russian literature is concerned, I am very fond of Tolstoy and Chekhov, and I also enjoy reading Gogol very much.
i-love-russian-classics-much-russian-classical-literature-but-i-also-read-modern-literature-as-far-as-russian-literature-is-concerned-i-am-fond-vladimir-putin
Literature was the passport to enter a larger life; that is, the zone of freedom. Literature was freedom. Especially in a time in which the values of reading and inwardness are so strenuously challenged, literature is freedom.
literature-was-passport-to-enter-larger-life-that-is-zone-freedom-literature-was-freedom-especially-in-time-in-which-values-reading-inwardness-are-strenuously-challenged-literatu
These studies are the result of my attempt to extract the essence of literature. Literature is either the essential or nothing. I believe that the Evil-an acute form of Evil-which it expresses, has a sovereign value for us. But this concept does not exclude morality: on the contrary, it demands a 'hypermorality.' Literature is communication. Communication requires loyalty. A rigorous morality results from complicity in the knowledge of Evil, which is the basis of intense communication. -Literature and Evil
these-studies-are-result-my-attempt-to-extract-essence-literature-literature-is-either-essential-nothing-i-believe-that-evil-acute-form-evilwhich-it-expresses-has-sovereign-value
For the judging of contemporary literature the only test is one's personal taste. If you much like a new book, you must call it literature even though you find no other soul to agree with you, and if you dislike a book you must declare that it is not literature though a million voices should shout you that you are wrong. The ultimate decision will be made by Time.
for-judging-contemporary-literature-only-test-is-ones-personal-taste-if-you-much-like-new-book-you-must-call-it-literature-even-though-you-find-no-ford-madox-ford
I'm kind of a reluctant Anglophile. My mother's a children's librarian, and all of the children's literature I read was from her childhood - E. Nesbit and Dickens, which isn't children's literature at all, but I was sort of steeped in English literature. I thought I was of that world.
Jefferson Mays
im-kind-reluctant-anglophile-my-mothers-childrens-librarian-all-childrens-literature-i-read-was-from-her-childhood-e-nesbit-dickens-which-isnt-childrens-literature-at-all-but-i-w
One task of literature is to formulate questions and construct counterstatements to the reigning pieties. And even when art is not oppositional, the arts gravitate toward contrariness. Literature is dialogue: responsiveness. Literature might be described as the history of human responsiveness to what is alive and what is moribund as cultures evolve and interact with one another.
one-task-literature-is-to-formulate-questions-construct-counterstatements-to-reigning-pieties-and-even-when-art-is-not-oppositional-arts-gravitate-susan-sontag
Fiction is a kind of compassion-generating machine that saves us from sloth. Is life kind or cruel? Yes, Literature answers. Are people good or bad? You bet, says Literature. But unlike other systems of knowing, Literature declines to eradicate one truth in favor of another.
fiction-is-kind-compassiongenerating-machine-that-saves-us-from-sloth-is-life-kind-cruel-yes-literature-answers-are-people-good-bad-you-bet-says-george-saunders
Our fiction is not merely in flight from the physical data of the actual world... it is, bewilderingly and embarrassingly, a gothic fiction, nonrealistic and negative, sadist and melodramatic - a literature of darkness and the grotesque in a land of light and affirmation... our classic [American] literature is a literature of horror for boys
Leslie Fielder
our-fiction-is-not-merely-in-flight-from-physical-data-actual-world-it-is-bewilderingly-embarrassingly-gothic-fiction-nonrealistic-negative-sadist-melodramatic-literature-darknes
Literature had torn Tessa and me apart, or prevented us from merging in the first place. That was its role in the world, I'd started to fear: to conjure up disagreements that didn't matter and inspire people to act on them as though they mattered more than anything. Without literature, humans would all be one. Warfare was simply literature in arms. The pen was the reason man invented the sword.
literature-had-torn-tessa-me-apart-prevented-us-from-merging-in-first-place-that-was-its-role-in-world-id-started-to-fear-to-conjure-up-disagreements-that-didnt-matter-inspire-pe
We were supposed to be an English literature class, but Miss Nesbitt used literature to teach real life. She said she didn't have time to teach us like a regular English teacher-we were too far behind. Instead, she taught us the world through literature.
Phillip M. Hoose
we-were-supposed-to-be-english-literature-class-but-miss-nesbitt-used-literature-to-teach-real-life-she-said-she-didnt-have-time-to-teach-us-like-regular-english-teacherwe-were-t
In the same period, Polish literature also underwent some significant changes. From social-political literature, which had a great tradition and strong motivation to be that way, Polish literature changed its focus to a psychological rather than a social one.
in-same-period-polish-literature-also-underwent-some-significant-changes-from-socialpolitical-literature-which-had-great-tradition-strong-andrzej-wajda
Books should confuse. Literature abhors the typical. Literature flows to the particular, the mundane, the greasiness of paper, the taste of warm beer, the smell of onion or quince. Auden has a line: "Ports have names they call the sea." Just so will literature describe life familiarly, regionally, in terms life is accustomed to use -- high or low matters not. Literature cannot by this impulse betray the grandeur of its subject -- there is only one subject: What it feels like to be alive. Nothing is irrelevant. Nothing is typical.
books-should-confuse-literature-abhors-typical-literature-flows-to-particular-mundane-greasiness-paper-taste-warm-beer-smell-onion-quince-richard-rodriguez
I see no reason in morality, why literature should not have as one of its intentions the arousing of thoughts of lust. It is one of the effects, perhaps one of the functions of literature to arouse desire, and I can discover no grounds for saying that sexual pleasure should not be among the objects of desire which literature presents to us, along with heroism, virtue, peace, death, food, wisdom, God, etc.
i-see-no-reason-in-morality-why-literature-should-not-have-as-one-its-intentions-arousing-thoughts-lust-it-is-one-effects-perhaps-one-lionel
Much, maybe too much, has been written about literature. (I know better than anyone; I'm an expert in the field). Yet the special thing about literature, the major art form of a Western civilization now ending before our very eyes, is not hard to define. Like literature, music can overwhelm you with sudden emotion, can move you to absolute sorrow or ecstasy; like literature, painting has the power to astonish, and to make you see the world through fresh eyes. But only literature can put you in touch with another human spirit, as a whole, with all its weaknesses and grandeurs, it limitations, its pettinesses, its obsessions, its beliefs; with whatever it finds moving, interesting, exciting, or repugnant. Only literature can grant you access to a spirit from beyond the grave-a more direct, more complete, deeper access than you'd have in conversation with a friend. Even in our deepest, most lasting friendships, we never speak so openly as when we face a blank page and address an unknown reader.
much-maybe-too-much-has-been-written-about-literature-i-know-better-than-anyone-im-expert-in-field-yet-special-thing-about-literature-major-art-form-western-civilization-now-endi
i-think-if-german-literature-could-survive-40s-russian-literature-could-survive-sovietism-american-literature-can-survive-google
To write is to forget. Literature is the most agreeable way of ignoring life. Music soothes, the visual arts exhilarates, the performing arts (such as acting and dance) entertain. Literature, however, retreats from life by turning in into slumber. The other arts make no such retreat- some because they use visible and hence vital formulas, others because they live from human life itself. This isn't the case with literature. Literature stimulates life. A novel is a story of what never was, a play is a novel without narration. A poem is the expression of ideas or feelings a language no one uses, because no one talks in verse.
to-write-is-to-forget-literature-is-most-agreeable-way-ignoring-life-music-soothes-visual-arts-exhilarates-performing-arts-such-as-acting-dance-entertain-literature-however-retre
English is, from my point of view as an Americanist, an ethnicity. And English literature should be studied in Comparative Literature. And American literature should be a discipline, certainly growing from England and France, Germany, Spain, Denmark, and the Native traditions, particularly because those helped form the American canon. Those are our backgrounds. And then we'd be doing it the way it ought to be done. And someday I hope that it will be.
english-is-from-my-point-view-as-americanist-ethnicity-and-english-literature-should-be-studied-in-comparative-literature-and-american-literature-paula-gunn-allen
Literature is the best way to overcome death. My father, as I said, is an actor. He's the happiest man on earth when he's performing, but when the show is over, he's sad and troubled. I wish he could live in the eternal present, because in the theater everything remains in memories and photographs. Literature, on the other hand, allows you to live in the present and to remain in the pantheon of the future.Literature is a way to say, I was here, this is what I thought, this is what I perceived. This is my signature, this is my name.
Ilan Stavans
literature-is-best-way-to-overcome-death-my-father-as-i-said-is-actor-hes-happiest-man-on-earth-when-hes-performing-but-when-show-is-over-hes-sad-ilan-stavans
Literature deals with morality but does not necessarily, does not, qua literature, help you to be more moral, either by precept or example. It makes you more aware. Which is to say that it makes you more human by making life more, not less, difficult. When you become more aware, the area of moral choice is widened. You can be a better man; you can also be a worse. Literature will not determine which. It is the equivalent of neither grace nor good works.
Eric Bentley
literature-deals-with-morality-but-does-not-necessarily-does-not-qua-literature-help-you-to-be-more-moral-either-by-precept-example-it-makes-you-more-aware-which-is-to-say-that-i
Literature differs from life in that life is amorphously full of detail, and rarely directs us toward it, wheras literature teaches us to notice. Literature makes us better noticers of life; we get to practice on life itself; which in turn makes us better readers of detail in literature; which in turn makes us better readers of life.
literature-differs-from-life-in-that-life-is-amorphously-full-detail-rarely-directs-us-toward-it-wheras-literature-teaches-us-to-notice-literature-makes-us-better-noticers-life-w
Literature can no longer be either Mimesis or Mathesis but merely Semiosis, the adventure of what is impossible to language, in a word: Text (it is wrong to say that the notion of 'text' repeats the notion of 'literature': literature represents a finite world, the text figures the infinite of language).
literature-can-no-longer-be-either-mimesis-mathesis-but-merely-semiosis-adventure-what-is-impossible-to-language-in-word-text-it-is-wrong-to-say-roland-barthes
What a lost person needs is a map of the territory, with his own position marked on it so he can see where he is in relation to everything else. Literature is not only a mirror; it is also a map, a geography of the mind. Our literature is one such map, if we can learn to read it as our literature, as the product of who and where we have been. We need such a map desperately, we need to know about here, because here is where we live. For the members of a country or a culture, shared knowledge of their place, their here, is not a luxury but a necessity. Without that knowledge we will not survive.
what-lost-person-needs-is-map-territory-with-his-own-position-marked-on-it-he-can-see-where-he-is-in-relation-to-everything-else-literature-is-margaret-atwood
To me, cinema is cinema. Cinema is one big tree with many branches. The same as literature. In literature, you don't just say, 'Oh, I bought some literature.' No, you say, 'I bought a novel' by so-and-so, or a book of essays by so-and-so.
to-me-cinema-is-cinema-cinema-is-one-big-tree-with-many-branches-the-same-as-literature-in-literature-you-dont-just-say-oh-i-bought-some-literature-no-you-say-i-bought-novel-by-b
If Freud turns to literature to describe traumatic experience, it is because literature, like psychoanalysis, is interested in the complex relation between knowing and not knowing, and it is at this specific point at which knowing and not knowing intersect that the psychoanalytic theory of traumatic experience and the language of literature meet.
Cathy Caruth
if-freud-turns-to-literature-to-describe-traumatic-experience-it-is-because-literature-like-psychoanalysis-is-interested-in-complex-relation-between-knowing-not-knowing-it-is-at-
When the critic has said everything in his power about a literary text, he has still said nothing; for the very existence of literature implies that it cannot be replaced by non-literature
when-critic-has-said-everything-in-his-power-about-literary-text-he-has-still-said-nothing-for-existence-literature-implies-that-it-cannot-be-replaced-by-nonliterature-tzvetan-to
you-can-travel-through-literature-you-can-expand-your-mind-through-literature-its-cheap-to-buy-that-kind-ticket-saul-williams
In some ways, getting published in children's literature is a little more open than publishing adult literature. It's less hinged on who you might know.
Marie Rutkoski
in-some-ways-getting-published-in-childrens-literature-is-little-more-open-than-publishing-adult-literature-its-less-hinged-on-who-you-might-know
the-attempt-to-devote-oneself-to-literature-alone-is-a-most-deceptive-thing-and-often-paradoxically-it-is-literature-that-suffers-for-it
I think all literature should be read as comparative literature. And I think we should write out of what we know, but in the expectation that we can be changed at any moment by something we have yet to discover.
Margo Jefferson
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Let us not kid ourselves; let us remember that literature is of no use whatever, except in the very special case of somebody's wishing to become, of all things, a Professor of Literature.
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Highlands, like Speyside, is in the north of Scotland. Some even have historically called Speyside a sub-region of the Highlands, and labels, such as Aberlour, sometimes blur the two. Highlands offers a diverse range of flavors, that often are noted by oak, fruit, smoke and floral notes.
To start with the obvious, Scotch – whether Speyside, the Highlands or of other regions – is aged in wood casks. Those casks can be of numerous origin too complicated to address here. But many, including many of those from the Speyside region, use used sherry casks during the maturation process. Sometimes, the whisky is stored exclusively in the sherry cask. Other times, the whisky is finished in sherry casks. Those casks can be blended together with non-sherry casks. And the sherry casks themselves can have different influences, based upon their origin, their age, the number of times they have been used, and their size, just to name a few. The point being, even sherry cask Scotches can take on widely different characteristics, but often the flavors imparted by sherry casks are sweet and fruity flavors.
July's Flight Club tasting features whiskies aged exclusive in sherry casks. And unlike many traditional Scotches, there are all bottled at cask strength – undiluted by flavorless water. The combination of the sherry cask and the cask strength is very richly fruited and complex whiskies.
Finally, what type of sherry casks were used, you might ask? Oloroso sherry is the most oft chosen cask, because that type of sherry typically produces a dry, full bodied fortified wine, with nutty and fruit flavors, and a background fruit sweetness. Most often, especially with older Oloroso sherries, the fruitiness is that of dark fruits.
Directions: Stir all ingredients with ice. Strain into a coupe glass. Rub lemon swath oils on rim of glass and as garnish.
This cocktail highlights the peculiar dryness/sweetness and fruitiness of the Oloroso sherry, while still allowing the delicate notes of the Scotch to shine through. The Benedictine D.O.M. and orange bitters add depth and complexity.
Nose: Dried sherry fruit of apricots, pears, orange peel, apple, plums, raisin and raspberry; wax; earth; cocoa and toffee; light baking spice.
Palate: Oak dryness and cinnamon followed by fruit punch, gummy bears and pear cider; spice; charred oak; leather. Rich but not overly viscus.
Finish: Long; dry oak; dried pear; dried sherry fruit; fruit leather; smoke and tobacco.
Why: This is a welcome introduction to sherry cask, cask strength Scotch. While the sherry fruits are strong, overall this has a fairly soft and balanced demeanor. It is complex, with dry character to offset sweetness.
Notes on Glenfarclas: Glenfarclas dates back to the early 1800 and remains one of the last family owned distilleries in Speyside. They are the last distillery in Scotland to use direct heating of the stills by gas. The Glenfarclas 105 is said to be the first cask strength Scotch. The 105 references the British proof system. Oloroso sherry is used for all of Glenfarclas' products.
Nose: Soft for its proof; stewed fruit; brown sugar; honey; baking spice; musty grape; faint dry oak; strawberry; banana; baked goods.
Palate: Developing baking spice; berry fruit jam; apple; pear; strawberry-banana; cinnamon toast; vanilla; spicy pepper. Creaminess that hits at the tail end of the palate and finish.
Finish: Thick and medium-long. Juicy ripe fruit; baked goods; vanilla; baking spice; white paper spice. There is a fruit leather texture that helps make the flavors linger.
Why: This whisky brings some spice and fresher fruitiness than the Glenfarclas 105. The fruits are quite contrasting: the Glenfarclas brings dried fruits, whereas this Glengoyne brings very fresh fruits.
Notes on Glengoyne: Glengoyne too has been operating since the early 1800's. Today it is owned by Ian MacLeod Distillers (as is the later Tamdhu). It sits on the line of the Highlands and the Lowlands regions of Scotland and is often said to be influenced by both styles. Glengoyne is not peated.
Nose: Berry/raisin heavy sherry fruit; oak; ginger; chocolate; vanilla; orange; fresh baked cake; nut.
Finish: Medium-long but slow fading. Nuts; cola; light brown sugar; plums; baking spice; baked goods.
Why: Tamdhu Batch Strength Batch 2 cracked the 2017 Top 10 on Whiskey Advocate. I've tried it. It is worth seeking out, but so are the other batches of Tamdhu. This whiskey is softer on the palate and finish than the others, but at 117.6 proof it isn't lacking in flavor.
Notes on Tamdhu: Located in the heart of Speyside, Tamdhu dates back to just before the 1900's. Its past is not as storied as many, but today is operated by Ian MacLeod Distillers to produce single malts.
Nose: A sherry bomb, with cooked and leather fruits (apple, berry; plum; grape, apricot); honey; leather; herbal/mint; tobacco; vanilla; caramel; some funky leather/oak dankness.
Palate: Rich and velvety; cooked fruits from the nose; juicy orange; caramel; vanilla; nuttiness; butter cream frosting.
Finish: Long. Leather; rich tobacco that weaves in and out of caramel and vanilla flavors; sherry; some smokey and metallic notes that hit on the back end.
Why: This is a single cask pick for Kansas by Standard Beverage. It can be picked up for around $55. I can't think of much better value in whiskey right now.
Notes on Glenrothes: Known most prominately as a distillery that produces whisky used in Cutty Sark and The Famous Grouse, Glenrothes also makes single malt whiskies. Most bottles of Glenrothes are bottled by vintage and not by age statement.
Nose: Brown butter; salted caramel; baking spice; vanilla; apple skins; salted chocolate; blackberry and raspberry; orange oils; pastry sweetness; leather.
Palate: Dried fruit medley (apples, black cherry; raspberries and blackberries); rye-like pepper spice; orange; baking spice; caramelized sugar; vanilla; salted chocolate. Incredibly rich, flavorful, and complex.
Finish: Long. Rich black cherry; dark chocolate; hints of salt and dried fruit throughout; sherry wood at the end.
Why: This is what most cask strength sherry cask Scotches are judged against. And this isn't even the best batch.
Notes on Aberlour: See our previous reviews of Aberlour 13, 16 and the A'Bunadh.


text:
Johanson–Blizzard syndrome
Johanson–Blizzard syndrome is a rare, sometimes fatal autosomal recessive multisystem congenital disorder featuring abnormal development of the pancreas, nose and scalp, with mental retardation, hearing loss and growth failure.[1] It is sometimes described as a form of ectodermal dysplasia.[2]
Johanson-Blizzard syndrome
The pancreas, and its location within the digestive system.
The disorder is especially noted for causing profound developmental errors and exocrine dysfunction of the pancreas, and it is considered to be an inherited pancreatic disease.[3]
PresentationEdit
ExocrineEdit
The most prominent effect of JBS is pancreatic exocrine insufficiency.[1][4][5][6][7] Varying degrees of decreased secretion of lipases, pancreatic juices such as trypsin, trypsinogen and others, as well as malabsorption of fats and disruptions of glucagon secretion and its response to hypoglycemia caused by insulin activity are major concerns when JBS is diagnosed.[1][3][8] Associated with developmental errors, impaired apoptosis, and both prenatal and chronic inflammatory damage, necrosis and fibrosis of the pancreatic acini (clusters of pancreatic exocrine gland tissue, where secretion of pancreatic juice and related enzymes occurs), pancreatic exocrine insufficiency in JBS can additionally stem from congenital replacement of the acini with fatty tissue.[1][3][8][9][10] Near total replacement of the entire pancreas with fatty tissue has also been reported. This is a progressive, sometimes fatal consequence of the disorder.[9]
EndocrineEdit
Endocrine insufficiency of the pancreas occurs with JBS, though it is sometimes less common and less pronounced than the more prominent effects on exocrine function.[1] The islets of Langerhans are ducts in the pancreas where endocrine activity such as the release of hormones glucagon, somatostatin and insulin takes place. Pancreatic endocrine insufficiency in JBS can be associated with either a buildup of connective tissue in the islet regions, congenital replacement of the islets with fatty tissue, or improper nerve signalling to the islets.[1][5][8][11][12] Endocrine dysfunction of the pancreas often results in diabetes mellitus. Both insulin resistance and diabetes have been observed with JBS, and it is suggested that diabetes should be considered as a complication of JBS and its course.[5][11]
Ductular output of fluids and electrolytes is preserved in the pancreas of many with JBS, as well as moderate to normal levels of functioning bicarbonate.[1]
Endocrine abnormalities in other areas have also been present with the disorder. These include hypothyroidism,[2] growth hormone deficiency[1][8] and hypopituitarism.[1] Findings affecting pituitary function in some JBS patients have included such anomalies as the formation of a glial hamartoma (a neoplasm, or tumor composed of glial cells) on a lobe of the pituitary gland, as well congenital underdevelopment of the anterior pituitary.[13] Growth failure and associated short stature (dwarfism) in JBS can be attributed to growth hormone deficiency caused by diminished anterior pituitary function, with malabsorption of fats playing a subsequent role.[1][4][14]
NasopharyngealEdit
Pharyngeal malformations can lead to food passing through the nose
The primary malformation apparent with JBS is hypoplasia (underdevelopment) of the nasal alae, or "wing of the nose".[1][2][7] Both hypoplasia and aplasia (partial or complete absence) of structural cartilage and tissue in this area of the nose, along with the underlying alae nasi muscle, are prevailing features of the disorder. Together, these malformations give the nose and nostrils an odd shape and appearance.[7][15]
NeurologicalEdit
Mental retardation ranging from mild to severe is present in the majority of JBS patients, and is related to the deleterious nature of the known mutagen responsible for the disorder and its effects on the developing central nervous system.[1][6][16] Normal intelligence and age appropriate social development, however, have been reported in a few instances of JBS.[12][16]
AuditoryEdit
Findings with the inner ear in JBS give explanation to the presence of bilateral sensorineural hearing loss in most patients affected by the disorder. The formation of cystic tissue in both the cochlea and vestibule, with resulting dilation (widening) and malformation of these delicate structures has been implicated.[7][9][17] Congenital deformations of the temporal bone and associated adverse anatomical effects on innervation and development of the inner ear also contribute to this type of hearing loss.[17][18]
CraniofacialEdit
Other abnormalities, affecting the scalp, head, face, jaw and teeth may be found with JBS. These include: ectodermal mid-line scalp defects with sparse, oddly-patterned hair growth;[2][9] aplasia cutis (underdeveloped, very thin skin) over the head,[19] an enlarged fontanelle ("soft spot" on the head of young infants),[14] microcephaly (undersized skull),[19] prominent forehead,[14] absence of eyebrows and eyelashes,[14] mongoloidal eye shape,[17] nasolacrimo-cutaneous fistulae (this refers to the formation of an abnormal secondary passageway from either the tear duct or lacrimal sac to the facial skin surface, possibly discharging fluid),[9] flattened ears,[14] micrognathism of the maxilla and mandible (underdevelopment of the upper and lower jaw, respectively), with the maxilla more prominently affected in some cases;[14][20][21] congenital clefting of bones surrounding the optical orbit (eye socket), such as the frontal and lacrimal bone;[20] and maldeveloped deciduous teeth ("baby teeth"), with an absence of permanent teeth.[9][14]
Effects on other organ systemsEdit
Additional congenital anomalies, effects on other organs, and less common features of JBS have included: imperforate anus (occlusion of the anus),[22] vesicoureteral reflux (reversal of the flow of urine, from the bladder back into the ureters, toward the kidneys);[14] duplex of the uterus and vagina in female infants,[7] neonatal cholestasis of the liver, with cirrhosis and portal hypertension (high blood pressure in the hepatic portal vein);[22] dilated cardiomyopathy,[23] dextrocardia (congenital displacement of the heart to the right side of the chest),[1] atrial and ventricular septal defect;[1] low birth-weight,[24] failure to thrive,[24] hypotonia (decreased muscle tone);[19] sacral hiatus (a structural deficiency of the sacral vertebrae),[24] congenital cataracts,[24] and cafe-au-lait spots.[2]
GeneticsEdit
Johanson-Blizzard syndrome has an autosomal recessive pattern of inheritance.
JBS is inherited in an autosomal recessive manner.[1] This means the defective gene responsible for the disorder is located on an autosome, and two copies of the defective gene (one inherited from each parent) are required in order to be born with the disorder. The parents of an individual with an autosomal recessive disorder both carry one copy of the defective gene, but usually do not experience any signs or symptoms of the disorder.[citation needed]
PathophysiologyEdit
Johanson–Blizzard syndrome is caused by mutations in the UBR1 gene, which encodes one of several ubiquitin ligase enzymes of the N-end rule pathway.[1][6]
The protein ubiquitin is a universal, "ubiquitously" expressed protein common to eukaryotic organisms. Ubiquitin plays a role in the regulation of other proteins by tagging them for eventual degradation by proteasomes.[25] This process begins when ubiquitin ligase covalently attaches a ubiquitin molecule to the lysine side chain of the target protein substrate (the misfolded, damaged, malfunctioning or unneeded protein that needs to be degraded). This is repeated a number of times in succession forming a chain of ubiquitin molecules, which is a process referred to as polyubiquitination. The polyubiquitination of the target protein signals the proteasome to break it down, which it does via proteolysis.[25] The ubiquitin-proteasome system plays a crucial role in the non-lysosomal degradation of intracellular proteins, and ubiquitin can also participate in modifying proteins to perform certain tasks.[25][26][27] Both degradation and modification of proteins within the cell are part of a broader regulatory scheme, necessary for cellular processes such as cell division, cell signalling, cell surface receptor function, apoptosis, DNA maintenance, inflammatory response and developmental quality control associated with the cell cycle and homeostasis in general.[26][27]
Ubiquitin-mediated degradation of proteins occurs through the N-end rule pathway.[28][29] In eukaryotes, including humans, the N-end rule pathway is part of the ubiquitin system.[28] Composed of a highly selective single-residue code (a single amino acid nucleotide sequence), the N-end rule serves as a mechanism which can relate the stability of a protein to the identity of the amino acid at its N-terminus (the end of the polypeptide with an amino group, which in the ubiquitin system may be involved in the reactive destabilization of the protein).[28][29][30]
In JBS, mutations in the UBR1 gene alter, disrupt or prevent the synthesis of ubiquitin ligase.[1][6] In the pancreatic acinar cells, UBR1 is more highly expressed than anywhere else in the body.[1] Impairment of the ubiquitin-proteasome system directly related to insufficient activity of ubiquitin ligase has been established as the cause of both congenital and progressive inflammatory damage, fatty tissue replacement, connective tissue proliferation and errors in innervation of the acini and islets, correlating to failures of normal apoptotic destruction of damaged cells and constitutive malpresence of proteins.[1][3][6] This also applies to other areas affected by deleterious UBR1 expression, such as the craniofacial area, musculoskeletal and nervous systems, dentition and organs.[1][6][22]
Missense, nonsense and splice site mutations of the UBR1 gene in both parents have been found with JBS, confirming the homozygous nature of the JBS phenotype. Variability of the phenotype, associated with residual ubiquitin ligase activity in some patients, has also been attributed to hypomorphic mutations occasionally found in either of the carrier parents.[1][3][6][22][23] The UBR1 gene is located on human chromosome 15.[6]
DiagnosisEdit
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TreatmentEdit
While there is no cure for JBS, treatment and management of specific symptoms and features of the disorder are applied and can often be successful. Variability in the severity of JBS on a case-by-case basis determines the requirements and effectiveness of any treatment selected.
Pancreatic insufficiency and malabsorption can be managed with pancreatic enzyme replacement therapy, such as pancrelipase supplementation and other related methods.[1]
Craniofacial and skeletal deformities may require surgical correction, using techniques including bone grafts and osteotomy procedures.[20] Sensorineural hearing loss can be managed with the use of hearing aids and educational services designated for the hearing impaired.[12][17]
Special education, specialized counseling methods and occupational therapy designed for those with mental retardation have proven to be effective, for both the patient and their families.[31] This, too, is carefully considered for JBS patients.
EponymEdit
Johanson–Blizzard syndrome was named after Ann J. Johanson and Robert M. Blizzard, the pediatricians who first described the disorder in a 1971 journal report.[15][32]
^ a b c d e f g h i j k l m n o p q r s t u v Alkhouri N, Kaplan B, Kay M, Shealy A, Crowe C, Bauhuber S, Zenker M (Nov 2008). "Johanson-Blizzard syndrome with mild phenotypic features confirmed by UBR1 gene testing". World Journal of Gastroenterology. 14 (44): 6863–6866. doi:10.3748/wjg.14.6863. PMC 2773884. PMID 19058315. Archived from the original (Free full text) on 2012-02-18.
^ a b c d e Kulkarni ML, Shetty SK, Kallambella KS, Kulkarni PM (Dec 2004). "Johanson--blizzard syndrome". Indian Journal of Pediatrics. 71 (12): 1127–1129. doi:10.1007/BF02829829. PMID 15630323.
^ a b c d e Zenker M, Mayerle J, Reis A, Lerch MM (Jun 2006). "Genetic basis and pancreatic biology of Johanson-Blizzard syndrome". Endocrinology and Metabolism Clinics of North America. 35 (2): 243–253, vii–viii. doi:10.1016/j.ecl.2006.02.013. PMID 16632090.
^ a b Sandhu BK, Brueton MJ (November 1989). "Concurrent pancreatic and growth hormone insufficiency in Johanson-Blizzard syndrome". J. Pediatr. Gastroenterol. Nutr. 9 (4): 535–8. doi:10.1097/00005176-198911000-00026. PMID 2621533.
^ a b c Steinbach WJ, Hintz RL (Nov 2000). "Diabetes mellitus and profound insulin resistance in Johanson-Blizzard syndrome". Journal of Pediatric Endocrinology & Metabolism : JPEM. 13 (9): 1633–1636. doi:10.1515/jpem.2000.13.9.1633. ISSN 0334-018X. PMID 11154160.
^ a b c d e f g h Zenker M, Mayerle J, Lerch MM, Tagariello A, Zerres K, Durie PR, Beier M, Hülskamp G, Guzman C, Rehder H, Beemer FA, Hamel B, Vanlieferinghen P, Gershoni-Baruch R, Vieira MW, Dumic M, Auslender R, Gil-Da-Silva-Lopes VL, Steinlicht S, Rauh M, Shalev SA, Thiel C, Ekici AB, Winterpacht A, Kwon YT, Varshavsky A, Reis A (Dec 2005). "Deficiency of UBR1, a ubiquitin ligase of the N-end rule pathway, causes pancreatic dysfunction, malformations and mental retardation (Johanson-Blizzard syndrome)" (PDF). Nature Genetics. 37 (12): 1345–1350. doi:10.1038/ng1681. PMID 16311597.
^ a b c d e Rosanowski F, Hoppe U, Hies T, Eysholdt U (Oct 1998). "Johanson-Blizzard syndrome. A complex dysplasia syndrome with aplasia of the nasal alae and inner ear deafness". HNO. 46 (10): 876–878. doi:10.1007/s001060050328. PMID 9846268.
^ a b c d Takahashi T, Fujishima M, Tsuchida S, Enoki M, Takada G (Aug 2004). "Johanson-blizzard syndrome: loss of glucagon secretion response to insulin-induced hypoglycemia". Journal of Pediatric Endocrinology & Metabolism : JPEM. 17 (8): 1141–1144. doi:10.1515/jpem.2004.17.8.1141. ISSN 0334-018X. PMID 15379429.
^ a b c d e f Daentl DL, Frías JL, Gilbert EF, Opitz JM (1979). "The Johanson-Blizzard syndrome: case report and autopsy findings". American Journal of Medical Genetics. 3 (2): 129–135. doi:10.1002/ajmg.1320030203. PMID 474625.
^ Jones NL, Hofley PM, Durie PR (Sep 1994). "Pathophysiology of the pancreatic defect in Johanson-Blizzard syndrome: a disorder of acinar development". The Journal of Pediatrics. 125 (3): 406–408. doi:10.1016/S0022-3476(05)83286-X. PMID 8071749.
^ a b Nagashima K, Yagi H, Kuroume T (Feb 1993). "A case of Johanson-Blizzard syndrome complicated by diabetes mellitus". Clinical Genetics. 43 (2): 98–100. doi:10.1111/j.1399-0004.1993.tb04458.x. ISSN 0009-9163. PMID 8448911.
^ a b c Gould NS, Paton JB, Bennett AR (Jun 1989). "Johanson-Blizzard syndrome: clinical and pathological findings in 2 sibs". American Journal of Medical Genetics. 33 (2): 194–199. doi:10.1002/ajmg.1320330212. PMID 2669481.
^ Hoffman WH, Lee JR, Kovacs K, Chen H, Yaghmai F (Jan 2007). "Johanson-Blizzard syndrome: autopsy findings with special emphasis on hypopituitarism and review of the literature". Pediatric and Developmental Pathology. 10 (1): 55–60. doi:10.2350/06-05-0085.1. PMID 17378628.
^ a b c d e f g h Fichter CR, Johnson GA, Braddock SR, Tobias JD (January 2003). "Perioperative care of the child with the Johanson-Blizzard syndrome". Paediatric Anaesthesia. 13 (1): 72–5. doi:10.1046/j.1460-9592.2003.00957.x. PMID 12535044.
^ a b Online Mendelian Inheritance in Man (OMIM) 243800
^ a b Moeschler JB, Polak MJ, Jenkins JJ, Amato RS (January 1987). "The Johanson-Blizzard syndrome: a second report of full autopsy findings". Am. J. Med. Genet. 26 (1): 133–8. doi:10.1002/ajmg.1320260120. PMID 3812553.
^ a b c d Braun J, Lerner A, Gershoni-Baruch R (1991). "The temporal bone in the Johanson-Blizzard syndrome. A CT study". Pediatric Radiology. 21 (8): 580–3. doi:10.1007/BF02012603. PMID 1815181.
^ Bamiou DE, Phelps P, Sirimanna T (March 2000). "Temporal bone computed tomography findings in bilateral sensorineural hearing loss". Arch. Dis. Child. 82 (3): 257–60. doi:10.1136/adc.82.3.257. PMC 1718255. PMID 10685935.
^ a b c Mardin MK, Ghandour M, Sakati NA, Nyhan WL (Nov 1978). "Johanson-Blizzard syndrome in a large inbred kindred with three involved members". Clin Genet. 14 (5): 247–250. doi:10.1111/j.1399-0004.1978.tb02141.x. PMID 709902.
^ a b c Kobayashi S, Ohmori K, Sekiguchi J (Sep 1995). "Johanson-Blizzard syndrome facial anomaly and its correction using a microsurgical bone graft and tripartite osteotomy". J Craniofac Surg. 6 (5): 382–385. doi:10.1097/00001665-199509000-00011. PMID 9020718.
^ Motohashi N, Pruzansky S, Day D (1981). "Roentgencephalometric analysis of craniofacial growth in the Johanson-Blizzard syndrome". J Craniofac Genet Dev Biol. 1 (1): 57–72. PMID 7341643.
^ a b c d Al-Dosari MS, Al-Muhsen S, Al-Jazaeri A, Mayerle J, Zenker M, Alkuraya FS (July 2008). "Johanson-Blizzard syndrome: report of a novel mutation and severe liver involvement". Am J Med Genet A. 146A (14): 1875–9. doi:10.1002/ajmg.a.32401. PMID 18553553.
^ a b Elting M, Kariminejad A, de Sonnaville ML, Ottenkamp J, Bauhuber S, Bozorgmehr B, Zenker M, Cobben JM (December 2008). "Johanson-Blizzard syndrome caused by identical UBR1 mutations in two unrelated girls, one with a cardiomyopathy". Am J Med Genet A. 146A (23): 3058–61. doi:10.1002/ajmg.a.32566. PMID 19006206.
^ a b c d Dumić M, Ille J, Bobonj G, Kordić R, Batinica S (May 1998). "Johanson-Blizzardov sindrom" [The Johanson-Blizzard syndrome]. Lijec Vjesn (in Croatian). 120 (5): 114–6. PMID 9748788.
^ a b c Wang J, Maldonado MA (August 2006). "The ubiquitin-proteasome system and its role in inflammatory and autoimmune diseases". Cell Mol Immunol. 3 (4): 255–61. PMID 16978533.
^ a b Ciechanover A (September 1994). "The ubiquitin-mediated proteolytic pathway: mechanisms of action and cellular physiology". Biol Chem Hoppe-Seyler. 375 (9): 565–81. doi:10.1515/bchm3.1994.375.8.565. PMID 7840898.
^ a b Ciechanover A, Iwai K (April 2004). "The ubiquitin system: from basic mechanisms to the patient bed". IUBMB Life. 56 (4): 193–201. doi:10.1080/1521654042000223616. PMID 15230346.
^ a b c Varshavsky A (January 1997). "The N-end rule pathway of protein degradation". Genes Cells. 2 (1): 13–28. doi:10.1046/j.1365-2443.1997.1020301.x. PMID 9112437.
^ a b Baker RT, Varshavsky A (February 1991). "Inhibition of the N-end rule pathway in living cells". Proc Natl Acad Sci USA. 88 (4): 1090–4. doi:10.1073/pnas.88.4.1090. PMC 50962. PMID 1899923.
^ Gonda DK, Bachmair A, Wünning I, Tobias JW, Lane WS, Varshavsky A (October 1989). "Universality and structure of the N-end rule". J Biol Chem. 264 (28): 16700–12. PMID 2506181.
^ Prater JF, D'Addio K (March 2002). "Johanson-Blizzard syndrome--a case study, behavioral manifestations, and successful treatment strategies". Biol Psychiatry. 51 (6): 515–7. doi:10.1016/S0006-3223(01)01337-3. PMID 11922888.
^ Johanson A, Blizzard R (December 1971). "A syndrome of congenital aplasia of the alae nasi, deafness, hypothyroidism, dwarfism, absent permanent teeth, and malabsorption". J Pediatr. 79 (6): 982–7. doi:10.1016/S0022-3476(71)80194-4. PMID 5171616.
ICD-10: Q87.8
ICD-9-CM: 751.7
MeSH: C535880
DiseasesDB: 31914
Retrieved from "https://en.wikipedia.org/w/index.php?title=Johanson–Blizzard_syndrome&oldid=906166178"


Good afternoon friends,Many time we are stuck up with strange issues in life.
Yesterday My Son came with a complain that he is annoyed by some other child time and time again . At very first I never react with such complains and I never try to complain to the teacher. But I have observed that there is one specific boy who is annoying my son frequently . I have first asked my son to complain about him to teacher. I learnt from him that teacher is not listening this stuff carefully.


This project started from my desire to add a pair of wide leg palazzo pants to my wardrobe. I wanted something fitted at the waist that was still flowy and comfortable, and settled on Burda 6906. The pattern suggested viscose or rayon crepe, so I went cruising through Mood fabrics selection of rayon crepes. I knew I wanted a print for these pants, and chose this green and ivory artistic rose stretch rayon crepe.
The care for this fabric was hand wash in cold water and line dry or dry clean. I do dry clean on occasion but not typically for casual clothing which these pants were intended to be. However, after putting the fabric through my machine's delicate cycle and hanging up to drip dry, the black started to run into the ivory and it looked terrible. I figured it wouldn't be useable to me that way and I had very little to lose by drying it in the dryer, so that's what I did (after washing on delicate again.) It came out exactly like it went in, and if I lost any of my original 2.5 yards to shrinking it wasn't evident when I was cutting out the pattern pieces.
The fit of these pants is just perfect right out of the envelope. I flat measured the waist since that measurement was not included on the pattern paper and went with the 10 instead of my typical woven size 12. I wasn't much worried about the hip measurement as this fabric has a good amount of stretch and they are pretty roomy through the hips as drafted.
I did try to match the roses on the print as best as I could, particularly at the center front and center back. The sides look okay – maybe not as perfect as I would like (especially on the right side) but really who is going to notice on these busy pants? Aren't you suppose to have a little imperfection somewhere to keep things interesting?
I really like the design of this fitted yoke lined in piping. The directions only instruct you to put it along the bottom of the yoke, but that didn't make much sense to me, so I stitched it to the top and bottom as per the envelope example.
I used knit interfacing on the yoke and yoke facing to give the pants some stability but still allow them to be stretchy and comfortable. The piping along the top acts like a waist stay and prevents that seam from stretching out. The back is closed with an invisible zipper.
This was such a fun project! I got the exact look I was going for, had no fit issues to speak of, enjoyed working with the fabric and my zipper went in perfectly the very first time (which pretty much never happens to me.) Definitely expect to see this pattern again soon, maybe the shorts view in a stretch denim chambray.


text:
Georg von Breitenbauch ist der Name folgender Personen:

* Georg August von Breitenbauch (1731–1817), deutscher Schriftsteller und Hofbeamter
 Georg Christoph von Breitenbauch (1658–1737), deutscher Rittergutsbesitzer und Hofbeamter

Siehe auch:
 Georg von Breitenbach (um 1485–1540/1541), deutscher Rechtsgelehrter und Kanzler
 Georg-Ludwig von Breitenbuch (* 1971), deutscher Politiker (CDU), MdL Sachsen

redpajama_set_name: RedPajamaWikipedia


Production has officially begun on the upcoming "Star Trek: Discovery" series and CBS All Access has released a behind-the-scenes featurette. Oooh is that an NX-inspired ship?
The new Starfleet uniforms seem to be a mix between the Enterprise-era uniforms and the TOS uniforms. Neat.
"Star Trek: Discovery" is set to release later in 2017.