Mad Cow Disease Hitting 'reset' in protein synthesis restores
myelination, suggests new treatment for misfolded protein
diseases (Medical Xpress)—A potential new treatment strategy for
patients with Charcot-Marie-Tooth disease is on the horizon,
thanks to research by neuroscientists now at the University at
Buffalo's Hunter James ... Medical research Apr 26, 2013 | 4.3 /
5 (4) | 0 | Bovine spongiform encephalopathy (BSE), commonly
known as mad-cow disease, is a fatal neurodegenerative disease
in cattle that causes a spongy degeneration in the brain and
spinal cord. BSE has a long incubation period, about 30 months
to 8 years, usually affecting adult cattle at a peak age onset
of four to five years, all breeds being equally susceptible. In
the United Kingdom, the country worst affected, more than
180,000 cattle have been infected and 4.4 million slaughtered
during the eradication program. The disease may be most easily
transmitted to human beings by eating food contaminated with the
brain, spinal cord or diges