What is Pulmonary Fibrosis? Pulmonary fibrosis is ongoing
scarring of the lungs that makes it increasingly more difficult
to breathe. "Fibrosis" is the medical term for scarring.
Idiopathic Interstitial Pneumonia (IIP) is a form of pulmonary
fibrosis and a subgroup of Interstitial Lung Disease (ILD). IIP
is a subgroup of interstitial lung disease. IPF is the most
common form of IIP. Click here for a larger picture. There are
many different forms of IIPs (see the picture above). The
different forms of IIPs are as follows: - Idiopathic Pulmonary
Fibrosis (IPF) - Non-Specific Interstitial Pneumonitis (NSIP) -
Cryptogenic Organizing Pneumonia (COP) - Lymphocytic
Interstitial Pneumonitis (LIP) - Respiratory Bronchiolitis
associated Interstitial Lung Disease (RB-ILD) - Desquamative
Interstitial Pneumonitis (DIP) - Acute Interstitial Pneumonia
(AIP) also called Hamman-Rich Syndrome Idiopathic Pulmonary
Fibrosis (IPF) is the most common form of IIP. Every year
approximately 48,000 individuals are diagnosed with IPF I