Gonadal dysgenesis is classified as any congenital developmental disorder of the reproductive system[1] in the male or female. It is the defective development of the gonads in an embryo,[2] with reproductive tissue replaced with functionless, fibrous tissue, termed streak gonads.[3] Streak gonads are a form of aplasia, resulting in hormonal failure that manifests as sexual infantism and infertility, with no initiation of puberty and secondary sex characteristics.[4]