Juvenile xanthogranuloma (JXG) is a rare dermatological disorder that primarily affects infants under one year of age but can also be found in older children and adults.[3] It was first described in 1905 by Adamson.[4] In 5% to 17% of patients, the disorder is present at birth, but the median age of onset is two years. JXG is a benign idiopathic cutaneous granulomatous tumor and the most common form of non-Langerhans cell histiocytosis (non-LHC).[3] The lesions appear as orange-red macules or papules and are usually located on the face, neck, and upper trunk. They may also appear at the groin, scrotum, penis, clitoris, toenail, palms, soles, lips, lungs, bone, heart, and gastrointestinal tract more rarely.[4] JXG usually manifests with multiple lesions on the head and neck in cases with children under six months of age.