Most commonly the melanocytoma is found on or adjacent to the optic nerve[7] as the optical melanocytoma. The lesion can be found at any age. Location and size could lead to clinical symptoms.While the melanocytoma is generally considered to be a benign tumor,[7] it has a potential for growth, recurrence, and transformation to a malignant melanoma.[5] Because malignant transformation is rare, optical melanocytomas can usually be observed.[1] Thus, in asymptomatic patients, regular observation by fundoscopy is indicated, perhaps supported by ocular ultrasonography.[8][5][10]