<p>This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.</p> <p>Biliary tact carcinoids are extremely rare: only ten cases have been reported up to now. The
Authors describe a successfully treated carcinoid tumour ofthe proximal bile duct and review the
literature about these rare malignancies.</p> <p>Despite extensive preoperative work-up, including ultrasound, CT scan and ERCP, a definite
diagnosis is hardly possible prior to histologic examination of the operative or necropsy
specimen.</p> <p>Due to the slow-growing nature and the non-aggressive behaviour of these malignancies,
surgical resection followed by biliodigestive anastomosis should be the treatment of choice.</p>
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HPB Surg. 1996; 9(2):101-105