title: Glycoproteinosis
text: # Glycoproteinosis
  
  Glycoproteinosis are lysosomal storage diseases affecting glycoproteins, resulting from defects in lysosomal function. The term is sometimes reserved for conditions involving degradation of glycoproteins.
  
  ## Types
  
  * (E77.0) Defects in post-translational modification of lysosomal enzymes
     * Mucolipidosis II (I-cell disease)
     * Mucolipidosis III (pseudo-Hurler polydystrophy)
  * (E77.1) Defects in glycoprotein degradation
     * Aspartylglucosaminuria
     * Fucosidosis
     * Mannosidosis
     * Sialidosis (mucolipidosis I)
  
  Another type, recently characterized, is galactosialidosis.
  
  