Upper urinary tract urothelial carcinoma (UTUC) is a rare malignant neoplasm arising from the urothelial lining of the renal collecting system and ureters. The current treatment paradigm for UTUC involves endoscopic resection, when technically feasible and oncologically sound, or complete resection of the kidney and ureter (nephroureterectomy) in cases in which organ-sparing treatment is not feasible.